Hartyánszky I

Bio: Hartyánszky I is an academic researcher from Gottsegen György Hungarian Institute of Cardiology. The author has contributed to research in topics: Ventricular outflow tract & Mitral valve. The author has an hindex of 4, co-authored 17 publications receiving 82 citations.

Rapid recurrence of an inflammatory myofibroblastic tumor in the right ventricular outflow tract.

Abstract: We describe an unusual case of rapid recurrence of a previously excised inflammatory myofibroblastic tumor of the right ventricular outflow tract in a 5-month-old infant The infant is asymptomatic 18 months after the second surgery The very rare cardiac involvement, and the early relapse of the inflammatory pseudotumor, to the best of our knowledge, is a unique combinationThe inflammatory myofibroblastic tumor, as known as a pseudotumor or plasma cell granuloma is an uncommon reactive lesion with unknown aetiology It is found most commonly in the lung and a number of visceral organs, such as the spleen, liver, ileum, salivary glands, urinary bladder, larynx or brain or in the retroperitoneum and lymph nodes To our knowledge only 9 cases have been published of such tumor arising within the heart1–6

Mitral valve anomalies obstructing left ventricular outflow

Abstract: This paper reports on two cases of more uncommon types of subaortic stenosis. A 2-year-old boy was found with accessory mitral valve leaflet (AMVL) attaching to the anterior leaflet, ballooning into the subaortic ventricular septum associated with a discrete subaortic membrane. The obstruction was successfully relieved by removal of the AMVL and resection of the membrane. A 19-day-old newborn with accessory tissue on the mitral valve (AMVT) causing subaortic stenosis, subaortic ventricular septal defect (VSD) and patent ductus arteriosus was operated on successfully. Accessory tissue excision through the VSD, VSD patch closure and ductus ligation were performed.

[Surgical management of congenital heart defects in adolescent and adult patients, between years 2001-2008].

Abstract: A felnőttkorban operalt veleszuletett szivhibak kozott vezetnek az I. rekonstrukcios beavatkozasok: a) frissen felismert betegsegek, b) megelőzően inoperabilisnak itelt korkepek, c) pulmonalis hypertonia, jobbkamra-elegtelenseg miatt „elkesett” műtetek. Novekszik a II. REDO műtetek szama: a) residuumok korrigalasa, b) kinőtt, diszfunkcios homograftok csereje, c) műteti/intervencios korrigalas utani recoarctatio (aneurysma, dissectio) sebeszete, d) aorta valvulotomia/valvuloplastica, illetve tarsvitiumok (TGA) korrigalasanak kovetkezmenyekent Ross-műtet, műbillentyű-beultetes . Betegek, eredmenyek: A 2001–2008 kozott vegzett 4496 műtet kozul 166 volt fiatal-felnőtt koru (16–52, atlageletkor: 28 ev) (Ia: 77, Ib: 15, Ic: 4, IIa: 11, IIb: 22, IIc: 9, IId: 28). Műteti mortalitas nem volt, 1 beteg pulmonalis hypertonias krizisben, 1 jobbkamra-elegtelenseg miatti malignus ritmuszavarban, 2 tobbszerv-elegtelensegben halt meg. Konkluzio: A rizikofaktorokat a pulmonalis hypertonia es a jobbkamra-elegtelenseg jelent...

Clinical, social, and ethical implications of changing life expectancy in Down syndrome

Abstract: Between 1 and 4% of the populations of developed nations are diagnosed with learning disability. In Australia, an estimated 1.9% of the population exhibit learning disability either as a primary disability or as a secondary condition, and approximately half of these people require continuing support in daily living, including mobility, self-care, and socialization. After improvements in basic public health measures, life expectancy in most developed nations increased over the course of the 20th century, and this trend included people with learning disability. Thus, by the end of that century, the survival estimates for people with mild learning disability living in developed countries was 70 years, and nearly 60 years of age for those with severe learning disability.

Cardiac inflammatory myofibroblastic tumor: a "benign" neoplasm that may result in syncope, myocardial infarction, and sudden death.

Abstract: Cardiac tumors other than myxomas are rare. We report a series of 10 intracavitary polypoid myofibroblastic proliferations in children and young adults emphasizing gross, histologic, and clinical features. There were 6 females and 4 males, with a mean age of 10 years (range 5 wk to 21 y). All lesions were endocardial-based, located in the right atrium (1), right ventricular inflow/tricuspid valve (1), right ventricular outflow (3), mitral valve (3), aortic valve/left coronary sinus (1), and left ventricular free wall (1). Symptoms included shortness of breath or dyspnea (3), syncope (2), chest pain (1), transient ischemic attacks (1), and fever with myalgias (1). All tumors were surgical resections, except 1 tumor that resulted in sudden coronary death and that was diagnosed at autopsy, and 1 tumor that embolized into the coronary artery and was treated by cardiac transplant. Two tumors, present in the aortic and mitral valves, respectively, caused cardiac ischemia. The tumors were polypoid or filiform and histologically resembled inflammatory myofibroblastic tumors of extracardiac sites, with loose spindle cell growth with sparse inflammation. Although there were frequent collagen bundles interspersed among the tumor cells, there were no large areas of dense fibrosis. Surface fibrin was present on the polypoid projections in 7 cases. Symptoms resulted from prolapse into coronary ostia or embolization, but no patient developed metastasis. Long-term follow-up in 2 patients demonstrated no evidence of disease or recurrence. Although metastatic potential was not identified, these tumors may result in serious symptoms, including myocardial infarct, syncope, and sudden death. These cardiac myofibroblastic tumors are readily distinguished from other endocardial-based cardiac tumors, including papillary fibroelastoma and myxoma, which may present clinically in the same manner.