Total anomalous pulmonary venous connection: Report of 93 autopsied cases with emphasis on diagnostic and surgical considerations.

Experience with 75 cases of proven total anomalous pulmonary venous connection without other significant cardiac malformations treated at the Children's Hospital Medical Center in Boston from Janua...

Total Anomalous Pulmonary Venous Connection Clinical and Physiologic Observations of 75 Pediatric Patients

Background:Total anomalous pulmonary venous connection (TAPVC) is a rare form of congenital heart disease. This study describes current surgical treatment strategies and experiences in a cohort of ...

Total Anomalous Pulmonary Venous Connection: The Current Management Strategies in a Pediatric Cohort of 768 Patients.

Eighty pathologic specimens with anomalies of pulmonary veins were reviewed for the type of lesions encountered. These were classified on an anatomic basis into five groups, characterized by (1) stenotic lesions; (2) accessory veins; and (3) anomalous connection of pulmonary veins (a) either partial or total, to a systemic vein or right atrium (the most common condition found), (b) to a systemic vein while connection to the arterial atrium was also present and (c) to a pulmonary artery (arteriovenous fistula). Combinations may occur, since pulmonary veins involved in anomalous connection may also be stenotic. The latter combination effects an adverse course on the patient with total anomalous pulmonary venous connection. The clinical manifestations of these malformations are dependent on the anatomic structure and in general result in one of three clinical pictures: (1) pulmonary venous obstruction, (2) bidirectional shunt and (3) cyanosis without abnormal cardiac signs.

Anomalies of the pulmonary veins

Congenital Heart Surgery Nomenclature and Database Project: pulmonary venous anomalies

Total pulmonary venous drainage into the right side of the heart; report of 17 autopsied cases not associated with other major cardiovascular anomalies.

W B Rothney

Papers

Total pulmonary venous drainage into the right side of the heart; report of 17 autopsied cases not associated with other major cardiovascular anomalies.