Congenital absence of the left pericardium. Clinical, electrocardiographic, radiographic, hemodynamic, and angiographic findings in six cases.
TLDR
It is suggested that partial pericardial defects may warrant surgical repair, and it is conceivable that a portion of the heart could herniate and transiently incarcerate through the partial defect during exercise.Abstract:
Until the past decade, the diagnosis of congenital absence of the pericardium, partial or complete, had rarely been made prior to postmortem examination or thoracotomy. Since 1963, the condition has been recognized during life in six patients at this institution. Of these six patients, two had partial absence of the left pericardium and four had complete absence of the left pericardium. Characteristic roentgenologic findings were present in all six patients. Associated heart lesions were not present in either patient with a partial pericardial defect. Two of the remaining four had associated heart lesions. One patient had surgical repair of an atrial septal defect. Surgical repair of the pericardial defect was not attempted in any of the six patients. Hemodynamic determinations at rest were normal in all six patients. The two patients with partial pericardial defects, however, had elevation of the pulmonary artery and left ventricular end-diastolic pressures during mild exercise in the recumbent position which suggests that this type of defect is not totally innocuous. In view of the unusual and extreme cardiac mobility in this condition, it is conceivable that a portion of the heart could herniate and transiently incarcerate through the partial defect during exercise. It is suggested that partial pericardial defects may warrant surgical repair. Small defects or complete absence of the left pericardium, however, are apparently without lethal potential and do not require surgical intervention.read more
Citations
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American Society of Echocardiography clinical recommendations for multimodality cardiovascular imaging of patients with pericardial disease: endorsed by the Society for Cardiovascular Magnetic Resonance and Society of Cardiovascular Computed Tomography.
Allan L. Klein,Suhny Abbara,Deborah A. Agler,Christopher P. Appleton,Craig R. Asher,Brian D. Hoit,Judy Hung,Mario J. Garcia,Itzhak Kronzon,Jae K. Oh,E. Rene Rodriguez,Hartzell V. Schaff,Paul Schoenhagen,Carmela D. Tan,Richard D. White +14 more
TL;DR: Allan L. Klein, MD, FASE, Chair, Suhny Abbara,MD, Deborah A. Agler, RCT, RDCS, Fase, Christopher P. Appleton, MD; Carmela D. Tan,MD; and Richard D.White, MD are the authors of this book.
Journal ArticleDOI
Pericardial Disease: Diagnosis and Management
Masud H. Khandaker,Raul E. Espinosa,Rick A. Nishimura,Lawrence J. Sinak,Sharonne N. Hayes,Rowlens M. Melduni,Jae K. Oh +6 more
TL;DR: The currently available evidence and the experiences from the pericardial clinic at the institution are represented to help guide the clinician in answering difficult diagnostic and management questions on pericARDial diseases.
Journal ArticleDOI
Isolated congenital absence of the pericardium: clinical presentation, diagnosis, and management
Michael A. Gatzoulis,Marc-David Munk,Naeem Merchant,Glen S. Van Arsdell,Brian W. McCrindle,Gary D. Webb +5 more
TL;DR: Isolated CAP has a common presentation pattern with periodic stabbing chest pain mimicking coronary artery disease, and Symptomatic patients with the complete form may benefit from pericardioplasty.
Journal ArticleDOI
Congenital partial and complete absence of the pericardium.
Jacques A.M. van Son,Gordon K. Danielson,Hartzell V. Schaff,Charles J. Mullany,Paul R. Julsrud,Jerome F. Breen +5 more
TL;DR: Between 1952 and 1991, 15 Mayo patients were found to have partial or complete absence of the pericardium at the time of a cardiovascular surgical procedure: three patients who underwent operation for complex congenital heart disease died, two early postoperatively and one late after a reoperation.
Journal ArticleDOI
Congenital absence of the pericardium: Echocardiography as a diagnostic tool
TL;DR: Between 1982 and 1992, 10 patients who underwent echocardiography at the Mayo Clinic were found to have congenital absence of the pericardium.
References
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Journal ArticleDOI
Congenital defects of the pericardium
TL;DR: Congenital deficiency of the pericardial sac has never been correctly diagnosed during life and is an anomaly which has aroused the attention largely of anatomists and embryologists, but in spite of its rarity it is not without clinical significance.
Journal ArticleDOI
Congenital pericardial defects.
TL;DR: One of the findings is of especial interest in that the defect was directly responsible for the death of the patient Such a result has been recorded on one previous occasion only.
Journal ArticleDOI
Congenital deficiency of the pericardium
Journal ArticleDOI
Congenital defect of the pericardium
TL;DR: The morbid anatomy and histopathology is described as found at necropsy on a 7-year-old coloured girl who suffered from partial defect of the pericardium with prolapse and partial incarceration of the cardiac apex.
Journal ArticleDOI
Congenital absence of the pericardium. A review of the literature with demonstration of a previously unreported fluoroscopic finding.
TL;DR: Of the 87 cases reviewed, congenital absence of the left pericardium (partial and total types) accounted for the vast majority of cases and was the method of choice for diagnosis.
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