Neurologic involvement in scleroderma: a systematic review.

Upon careful examination, 23 of 24 patients with progressive systemic sclerosis (PSS) were found to have abnormalities of muscle. Nineteen patients presented a homogenous pattern of muscle abnormalities, which untreated was associated with a stable course ("simple myopathy"). Three patients demonstrated inflammatory muscle disease indistinguishable from polymyositis while a fourth patient developed marked weakness associated with a generalized neuropathic process. Muscle enzymes, electromyogram, and muscle biopsy permitted distinction among the different muscle disorders, a distinction that could have prognostic and therapeutic importance.

https://onlinelibrary.wiley.com/doi/pdf/10.1002/art.1780210111

Muscle disease in progressive systemic sclerosis. diagnostic and therapeutic considerations

Electromyographic findings were studied in 32 women and 7 men with progressive systemic sclerosis. Among the 14 patients in group 1, 7 had the CREST syndrome in an early stage while the 14 patients in group 2 had advanced CREST-type lesions. The 18 patients in group 3 had diffuse scleroderma with extensive visceral involvement. In all groups, the mean duration of single potentials was reduced and the percent of polyphasic potentials was above normal in groups 2 and 3. Distal muscles were more involved in group 1, and proximal muscles in group 2. In group 3, involvement of various muscles was nearly equal. Electromyographic changes correlated with the clinical condition of the patients. Overall, the findings in this study are similar to findings from other laboratories.

https://www.onlinelibrary.wiley.com/doi/pdf/10.1002/art.1780250110

Electromyographic findings in various forms of progressive systemic sclerosis

Histopathological features of systemic sclerosis-associated myopathy: A scoping review.

Presentation of Case A 77-year-old man was admitted to the hospital because of weakness. Five years previously congestive heart failure occurred, and atrial fibrillation was found. There was a sing...

Case 33-1973

The authors discuss the electromyographic findings in generalized scleroderma on the basis of 64 cases.

Irena Hausmanowa-Petrusewicz

Papers

Further studies on electromyographic findings in generalized scleroderma.