Showing papers by "Kapil D. Sethi published in 1988"
TL;DR: Two women with a presumptive diagnosis of Hallervor‐den‐Spatz syndrome had a combination of dystonia and parkinsonism and one had retinitis pigmentosa, and magnetic resonance imaging showed striking abnormalities in the globus pallidus bilaterally.
Abstract: Two women with a presumptive diagnosis of Hallervor-den-Spatz syndrome had a combination of dystonia and parkinsonism. One had retinitis pigmentosa. Neuropsychological testing revealed Decemberreased verbal fluency and visuoconstructional and motor deficits. Magnetic resonance imaging performed with a high-field-strength unit (1.5 Tesla) showed striking abnormalities in the globus pallidus bilaterally (“eye-of-the-tiger” sign). Magnetic resonance imaging may prove useful in the diagnosis of Hallervorden-Spatz syndrome.
200 citations