P
Paolo Ciliberti
Researcher at Boston Children's Hospital
Publications - 42
Citations - 2287
Paolo Ciliberti is an academic researcher from Boston Children's Hospital. The author has contributed to research in topics: Heart disease & Population. The author has an hindex of 12, co-authored 37 publications receiving 1661 citations. Previous affiliations of Paolo Ciliberti include University of Bologna & Great Ormond Street Hospital.
Papers
More filters
Journal ArticleDOI
Noninvasive Etiologic Diagnosis of Cardiac Amyloidosis Using 99mTc-3,3-Diphosphono-1,2-Propanodicarboxylic Acid Scintigraphy
Enrica Perugini,Pier Luigi Guidalotti,Fabrizio Salvi,Robin M. T. Cooke,Cinzia Pettinato,Letizia Riva,Ornella Leone,Mohsen Farsad,Paolo Ciliberti,Letizia Bacchi-Reggiani,Francesco Fallani,Angelo Branzi,Claudio Rapezzi +12 more
TL;DR: It is concluded that 99mTc-DPD scintigraphy is a useful step in the workup of the differential diagnosis of TTR versus AL etiology in patients with documented cardiac amyloidosis.
Journal ArticleDOI
Systemic Cardiac Amyloidoses Disease Profiles and Clinical Courses of the 3 Main Types
Claudio Rapezzi,Giampaolo Merlini,Candida Cristina Quarta,Letizia Riva,Simone Longhi,Ornella Leone,Fabrizio Salvi,Paolo Ciliberti,Francesca Pastorelli,Elena Biagini,Fabio Coccolo,Robin M. T. Cooke,Letizia Bacchi-Reggiani,Diego Sangiorgi,Alessandra Ferlini,Michele Cavo,Elena Zamagni,Maria Luisa Fonte,Giovanni Palladini,Francesco Salinaro,Francesco Musca,Laura Obici,Angelo Branzi,Stefano Perlini +23 more
TL;DR: AL, ATTRm, and ATTRwt should be considered 3 different cardiac diseases, probably characterized by different pathophysiological substrates and courses.
Journal ArticleDOI
Transthyretin-related amyloidoses and the heart: a clinical overview
Claudio Rapezzi,Candida Cristina Quarta,Letizia Riva,Simone Longhi,Ilaria Gallelli,Massimiliano Lorenzini,Paolo Ciliberti,Elena Biagini,Fabrizio Salvi,Angelo Branzi +9 more
TL;DR: Clinicians should consider the possibility of ATTR in all patients who present with an unexplained increase in left ventricular wall thickness at echocardiography, and should include an active search for possible red flags that can point to the correct final diagnosis.
Journal ArticleDOI
Acute Cardiovascular Manifestations in 286 Children with Multisystem Inflammatory Syndrome Associated with COVID-19 Infection in Europe.
Israel Valverde,Yogen Singh,Joan Sanchez-de-Toledo,Paraskevi Theocharis,Ashish Chikermane,Sylvie Di Filippo,Beata Kucińska,Savina Mannarino,Amalia Tamariz-Martel,Federico Gutierrez-Larraya,Giridhar Soda,Kristof Vandekerckhove,Francisco Gonzalez-Barlatay,Colin J. McMahon,Simona Anna Marcora,Carlo Pace Napoleone,Phuoc Duong,Giulia Tuo,Antigoni Deri,Gauri Nepali,Maria Ilina,Paolo Ciliberti,Owen Miller,Xavier Iriart,Jelena Hubrechts,Irene M. Kuipers,Ana R. Sousa,Andrea Donti,Abigail Sharpe,Zdenka Reinhardt,Francesca Cairello,Daniël De Wolf,Marisa Vieira,Cecilia Lazea,Ferran Gran,Constancio Medrano-Lopez,Almudena Ortiz-Garrido,Vladislav Vukomanovic,Bernadette Brent,Ornella Milanesi,Wendy Dewals,Begoña Manso,Emanuela Valsangiacomo-Buchel,Andreia Francisco,Marie-Christine Seghaye,Isabelle Loeckx,Moises Rodriguez-Gonzalez,Susana Maria Rey-García,Victoria C. Ziesenitz,Giulia Bordin,Gabriela Doros,Gernot Grangl,Shalan Uaid Fadl,Karl Viktor Perminow,Fernando Centeno,Fatima Pinto,Jussi Niemelä,Hari Krishnan Kanthimathinathan,Paula C Randanne,Cezary Niszczota,Gian Vincenzo Zuccotti,Inés Leoz Gordillo,Madhu Obeyasekhara,Catherine Armstrong,Karina Butler,Matteo Ciuffreda,Anna Maria Villar,Naga Pappula,Roberta Caorsi,Davinder Singh,Saravanan Durairaj,Karen McLeod,Giulio Calcagni,Youssef Quizad,Marc Gewillig,Taco W. Kuijpers,Rita Ataide,Marianna Fabi,Tara Bharucha,Khushnood Abbas,Silvia Alessandra Magrass,James Wong,Daniela Iacob,Joan Balcells,Nuria GilVillanueva,Victorio Cuenca-Peiro,Ivana Cerovi,Avishay Sarfatt,Mahmoud Zaqout,Elia Sanchez-Valderrabanos,Janet Kelly-Geyer,Faim Diogo,Nathalie Cajgfinger,Mascart Françoise,Fernando Rueda-Nuñez,Matthias Gorenflo,Alessandra Grison,Delia Mihailov,Martin Koestenberger,Carlos Alcalde,Conceiçao Trigo,Anita Arola,Katarina Hanséus +102 more
TL;DR: Compared to adults with Covid-19, mortality in children with MIS-C is uncommon despite multi-system involvement, very elevated inflammatory markers and need for intensive care support.
Journal ArticleDOI
Gender-related risk of myocardial involvement in systemic amyloidosis
Claudio Rapezzi,Letizia Riva,Cristina Quarta,Enrica Perugini,Fabrizio Salvi,Simone Longhi,Paolo Ciliberti,Francesca Pastorelli,Elena Biagini,Ornella Leone,Robin M. T. Cooke,Letizia Bacchi-Reggiani,Alessandra Ferlini,Michele Cavo,Giampaolo Merlini,Stefano Perlini,Sonia Pasquali,Angelo Branzi +17 more
TL;DR: The hypothesis that some biological characteristic associated with female gender protects against myocardial involvement in familial ATTR is raised, as well as the possible role of female sex hormones by considering menopausal status.