Displasia arritmogénica del ventrículo derecho con compromiso de ventrículo izquierdo: valor diagnóstico de la resonancia cardiaca
Rienzi Díaz,Danilo Silva +1 more
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TLDR
Two patients with ventricular tachycardia due to arrhythmogenic right ventricular dysplasia are reported, one of which is a 49 year-old female with a history of ventricularTachycardIA and the other is a 37-year-old male admitted for recurrent syncope.Abstract:
Arrhythmogenic right ventricular dysplasia is an inherited condition characterized by replacement of normal myocardium by fatty or fibro-fatty tissue, which mainly affects the right ventricle. The most frequent form of presentation is ventricular tachycardia or sudden death, whose origin is considered to be a product of fibrous or fatty infiltration of the myocardium. This structural damage can be detected by cardiac magnetic resonance imaging (MR). We report two patients with ventricular tachycardia due to arrhythmogenic right ventricular dysplasia. A 49 year-old female with a history of ventricular tachycardia. EKG showed epsilon waves and a prolonged QTc. Echocardiogram showed right ventricular dilatation and dysfunction. MR showed right ventricular fatty infiltration. An implantable cardioverter-defibrillator was installed to the patient. A 37 year-old male was admitted for recurrent syncope. On admission a ventricular tachycardia was detected. An echocardiogram showed right ventricular dilatation and dysfunction. MR showed a large zone of fibrosis in the right ventricle. An implantable cardioverter-defibrillator was also installed.read more
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Journal ArticleDOI
Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia
Frank I. Marcus,William J. McKenna,Duane L. Sherrill,Cristina Basso,Barbara Bauce,David A. Bluemke,Hugh Calkins,Domenico Corrado,Moniek G.P.J. Cox,James P. Daubert,Guy Fontaine,Kathleen Gear,Richard N.W. Hauer,Andrea Nava,Michael H. Picard,Nikos Protonotarios,Jeffrey E. Saffitz,Danita M. Yoerger Sanborn,Jonathan S. Steinberg,Harikrishna Tandri,Gaetano Thiene,Jeffrey A. Towbin,Adalena Tsatsopoulou,Thomas Wichter,Wojciech Zareba +24 more
TL;DR: The criteria for the clinical diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia have been modified to incorporate new knowledge and technology to improve diagnostic sensitivity, but with the important requisite of maintaining diagnostic specificity.
Journal ArticleDOI
Right ventricular dysplasia: a report of 24 adult cases.
Frank I. Marcus,Guy Fontaine,Gerard M. Guiraudon,Robert T. Frank,Jean L. Laurenceau,Christine Malergue,Yves Grosgogeat +6 more
TL;DR: A unique experience, when combined with a literature review of 34 adult cases, permits a composite clinical profile of this condition in the adult, and shows increased right ventricular diastolic dimensions in patients with recurrent ventricular tachycardia.
Journal ArticleDOI
Spectrum of Clinicopathologic Manifestations of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: A Multicenter Study
Domenico Corrado,Cristina Basso,Gaetano Thiene,William J. McKenna,Michael J. Davies,Fontaliran F,Andrea Nava,Furio Silvestri,Carina Blomström-Lundqvist,Elżbieta K. Włodarska,Guy Fontaine,Fulvio Camerini +11 more
TL;DR: Spectrum of Clinicopathologic Manifestations of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: A Multicenter study as mentioned in this paper was conducted to investigate the effect of arrhythmogenic right ventricular arrhythmia.
Journal ArticleDOI
Implantable Cardioverter-Defibrillator Therapy for Prevention of Sudden Death in Patients With Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia
Domenico Corrado,Loira Leoni,Mark S. Link,Paolo Della Bella,Fiorenzo Gaita,Antonio Curnis,Jorge Uriarte Salerno,Diran Igidbashian,Antonio Raviele,Marcello Disertori,Gabriele Zanotto,Roberto Verlato,Giuseppe Vergara,Pietro Delise,P. Turrini,Cristina Basso,Franco Naccarella,Maddalena F,N.A. Mark Estes,Gianfranco Buja,Gaetano Thiene +20 more
TL;DR: In patients with ARVC/D, ICD therapy provided life-saving protection by effectively terminating life-threatening ventricular arrhythmias as well as identifying patients who were prone to ventricular fibrillation/flutter on the basis of clinical presentation.
Journal ArticleDOI
Noninvasive detection of myocardial fibrosis in arrhythmogenic right ventricular cardiomyopathy using delayed-enhancement magnetic resonance imaging
Harikrishna Tandri,Manoj Saranathan,E. Rene Rodriguez,Claudia Martinez,Chandra Bomma,Khurram Nasir,Boas Rosen,Joao A.C. Lima,Hugh Calkins,David A. Bluemke +9 more
TL;DR: In this paper, the role of myocardial delayedenhancement (MDE) magnetic resonance imaging (MRI) for noninvasive detection of fibrosis in ARVD/C was evaluated.