Journal ArticleDOI
Hemorrhagic Diathesis Associated With Benign Histiocytic, Cytophagic Panniculitis and Systemic Histiocytosis
Reads0
Chats0
TLDR
Five patients had a histiocytic, cytophagic panniculitis and a febrile, progressive course, which included hepatosplenomegaly, pancytopenia, liver function abnormalities, and a hemorrhagic death, and the terminal hemorrhage was characterized by features of intravascular coagulation and liver failure.Abstract:
• Five patients had a histiocytic, cytophagic panniculitis and a febrile, progressive course, which included hepatosplenomegaly, pancytopenia, liver function abnormalities, and a hemorrhagic death. The terminal hemorrhage was characterized by features of intravascular coagulation and liver failure. The histiocytosis could be found at times also in bone marrow, lymph nodes, liver and spleen, and serosal tissues, as well as in skin and subcutaneous tissue. Adequate biopsy diagnosis will prevent such cases from being labeled as Weber-Christian disease with bleeding, and offer an opportunity for appropriate treatment of this new syndrome of histiocytic, cytophagic panniculitis. (Arch Intern Med140:1460-1463, 1980)read more
Citations
More filters
Journal ArticleDOI
Panniculitis. Part II. Mostly lobular panniculitis.
TL;DR: Participants in this learning activity should be familiar with the pathogenesis, clinical manifestations, histopathologic findings, and treatment options for the most frequent variants of the lobular panniculitis.
Journal ArticleDOI
Primary cutaneous lymphomas: applicability of current classification schemes (European Organization for Research and Treatment of Cancer, World Health Organization) based on clinicopathologic features observed in a large group of patients.
TL;DR: The study confirmed that the EORTC classification allows a better management of patients with PCL and small amendments to that classification should be carried out to account for recently described entities and to unify some of the diagnostic categories.
Journal ArticleDOI
Hemophagocytic syndromes (HPSs) including hemophagocytic lymphohistiocytosis (HLH) in adults: A systematic scoping review.
TL;DR: The aims of this systematic scoping review were to provide an overview of existing literature on adult HPS/HLH, describe current practices in diagnosis and treatment, and propose priorities for future research.
Journal ArticleDOI
Hemophagocytic lymphohistiocytosis: a hemophagocytic syndrome.
TL;DR: Hemophagocytic lymphohistiocytosis, terminology that designates a syndrome that may be familial or sporadic, with or without an associated viral infection, is presented as the prototype of a hemophgocytic syndrome, a condition in which there is uncontrolled activation of the cellular immune system.
Journal ArticleDOI
Lupus profundus, indeterminate lymphocytic lobular panniculitis and subcutaneous T‐cell lymphoma: a spectrum of subcuticular T‐cell lymphoid dyscrasia
TL;DR: This work encountered 32 cases of primary LLP which could be categorized as: 1) lupus erythematosus profundus (LEP) (19 patients); 2) an indeterminates group termed indeterminate lymphocytic lobular panniculitis (ILLP); and 3) subcutaneous T‐cell lymphoma (SCTCL) (7 patients).
References
More filters
Book
Tumors of the hematopoietic system
TL;DR: Reading tumors of the hematopoietic system is also a way as one of the collective books that gives many advantages.
Journal ArticleDOI
Histiocytic medullary reticulosis
TL;DR: A case typical of histiocytic medullary reticulosis with chest pain as the presenting complaint is observed and would like to add this case to the small number previously reported.
Journal ArticleDOI
Malignant histiocytosis (histiocytic medullary reticulosis). I. Clinicopathologic study of 29 cases
TL;DR: The clinical records and histologic materials from 29 cases of malignant histiocytosis have been reviewed, as well as autopsy findings in 14 cases, and bone marrow aspiration was superior to biopsy in assessing marrow involvement.
Journal ArticleDOI
Histiocytic medullary reticulosis. Report of two cases and review of the literature.
Donald C. Abele,Tommy B. Griffin +1 more
TL;DR: Although there are similarities of histiocytic medullary reticulosis to Hodgkin's disease, Letterer-Siwe disease, and lymphomatous diseases, it is thought that histuocytic Medullary ReticULosis is a distinct clinicopathologic type of malignant Histiocytosis.