O
Olivier Albaric
Researcher at Université Nantes Angers Le Mans
Publications - 2
Citations - 45
Olivier Albaric is an academic researcher from Université Nantes Angers Le Mans. The author has contributed to research in topics: Mitochondrial carrier & Ataxia. The author has an hindex of 2, co-authored 2 publications receiving 34 citations.
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Progressive ataxia of Charolais cattle highlights a role of KIF1C in sustainable myelination
Amandine Duchesne,Anne Vaiman,Magali Frah,Sandrine Floriot,Sabrina Legoueix-Rodriguez,Sabrina Legoueix-Rodriguez,Anne Desmazières,Sébastien Fritz,Christian Beauvallet,Olivier Albaric,Eric Venot,Maud Bertaud,Romain Saintilan,Raphaël Guatteo,Diane Esquerre,Julien Branchu,Anaïs Fleming,Alexis Brice,Frédéric Darios,Jean-Luc Vilotte,Giovanni Stevanin,Didier Boichard,Khalid Hamid El Hachimi +22 more
TL;DR: This model highlights the role of KIF1C protein in preserving the structural integrity and function of myelin, since the clinical signs and lesions arise in young-adult Charolais cattle, and provides useful information for SPG58/SPAX2 disease and other demyelinating lesions.
Journal ArticleDOI
Bovine and murine models highlight novel roles for SLC25A46 in mitochondrial dynamics and metabolism, with implications for human and animal health.
Amandine Duchesne,Anne Vaiman,Johan Castille,Christian Beauvallet,Pauline Gaignard,Sandrine Floriot,Sabrina Rodriguez,Sabrina Rodriguez,Marthe Vilotte,Laurent Boulanger,Bruno Passet,Olivier Albaric,François Guillaume,Abdelhak Boukadiri,Laurence Richard,Maud Bertaud,Edouard Timsit,Raphaël Guatteo,Florence Jaffrezic,Pierre Calvel,Louise Helary,Rachid Mahla,Diane Esquerre,Christine Péchoux,Sophie Liuu,Jean-Michel Vallat,Didier Boichard,Abdelhamid Slama,Jean-Luc Vilotte +28 more
TL;DR: It is shown that the Slc25a46 disruption caused a fusion/fission imbalance and an abnormal mitochondrial architecture that disturbed mitochondrial metabolism, resulting in premature mortality.