Journal ArticleDOI
Long-Term Follow-up of Nocturnal Ventilatory Assistance in Patients with Respiratory Failure Due to Duchenne-Type Muscular Dystrophy
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TLDR
It is concluded that noninvasive intermittent ventilatory assistance effectively reverses hypoventilation and symptoms in patients with late-stage Duchenne muscular dystrophy, but pulmonary function continues to deteriorate necessitating longer periods of ventilation, and often tracheostomy, within a few years.About:
This article is published in Chest.The article was published on 1990-01-01. It has received 58 citations till now. The article focuses on the topics: Pulmonary function testing & Duchenne muscular dystrophy.read more
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Journal ArticleDOI
Impact of nasal ventilation on survival in hypercapnic Duchenne muscular dystrophy
TL;DR: Nal ventilation is likely to increase survival in hypercapnic patients with Duchenne muscular dystrophy and should be considered as a treatment option when ventilatory failure develops, according to this study.
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Daytime predictors of sleep hypoventilation in Duchenne muscular dystrophy.
Craig A. Hukins,David R. Hillman +1 more
TL;DR: It is concluded that in patients with DMD, arterial blood gases should be performed once the FEV(1) falls below 40% of the predicted value, as the NIV-associated decrease in wakeful Pa(CO(2)) occurs despite a further decline in ventilatory capacity, suggesting continuing deterioration in respiratory muscle function.
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Noninvasive Positive Pressure Ventilation To Treat Respiratory Failure
Thomas J. Meyer,Nicholas S. Hill +1 more
TL;DR: Use of noninvasive positive pressure ventilation, the delivery of positive pressure mechanical ventilation to the lungs without endotracheal intubation, is increasing among patients with acute and chronic respiratory failure, mainly because of its convenience, lower cost, and morbidity-sparing potential compared with standard invasive positive Pressure ventilation.
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Longterm noninvasive ventilation in children and adolescents with neuromuscular disorders
TL;DR: Noninvasive (positivepressure) ventilation has favourable longterm impact on nocturnal and diurnal gas exchange and sleep and in patients with nonDuchenne neuromuscular disorders on vital capacity as well.
Journal ArticleDOI
Long-term Nasal Intermittent Positive Pressure Ventilation in Advanced Duchenne's Muscular Dystrophy
TL;DR: These are the first comparative results confirming that long-term NIPPV helps to stabilize pulmonary function and to prolong the expectancy of life of patients with DMD.
References
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Principles and Procedures of Statistics.
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Pulmonary function in Duchenne muscular dystrophy related to stage of disease
TL;DR: Pulmonary function studies, particularly of blood gases in conjunction with functional class, may be a significant help in estimating the prognosis and in determining the intensity of acute care in patients in whom pulmonary infection or symptoms of respiratory failure develop.
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Practical problems in the respiratory care of patients with muscular dystrophy.
TL;DR: A large number of patients with these dystrophies have severe central giant cell granuloma, which is known to be a major source of central nervous system damage and organ failure.
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Nocturnal positive pressure ventilation via nasal mask.
TL;DR: Five patients with chronic respiratory failure from neuromuscular disease and symptomatic worsening nocturnal hypoventilation were treated withNocturnal ventilatory support, and symptoms of headache, insomnia/somnolence, and impaired intellectual capacity rapidly disappeared.