Journal•ISSN: 1569-1993
Journal of Cystic Fibrosis
Elsevier BV
About: Journal of Cystic Fibrosis is an academic journal published by Elsevier BV. The journal publishes majorly in the area(s): Cystic fibrosis & Medicine. It has an ISSN identifier of 1569-1993. Over the lifetime, 5519 publications have been published receiving 71810 citations.
Topics: Cystic fibrosis, Medicine, Internal medicine, Biology, Ivacaftor
Papers published on a yearly basis
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TL;DR: The validity and importance of identifying these four subgroups of patients as either 'chronic', 'intermittent', 'free of PA', or 'never infected' is demonstrated.
585 citations
Katholieke Universiteit Leuven1, Charles University in Prague2, University of Toronto3, University of Verona4, French Institute of Health and Medical Research5, Johns Hopkins University6, Swansea University7, Boston Children's Hospital8, Medical Products Agency9, Hebrew University of Jerusalem10, University of North Carolina at Chapel Hill11, St Mary's Hospital12, Hochschule Hannover13, Athens State University14, Queen's University Belfast15
TL;DR: The conclusions of a consensus conference to address the use and interpretation of CF mutation analysis in clinical settings are described, including the use of CFTR genotype for prediction of prognosis in people with CF at the time of their diagnosis is not recommended.
545 citations
TL;DR: The clinical consequences include multi-system disease characterised by progressive pulmonary damage leading to respiratory failure, pancreatic dysfunction, liver disease that may progress to cirrhosis, gut motility problems, and elevated sweat electrolytes.
468 citations
TL;DR: This document is the result of an European Consensus conference which took place in Artimino, Tuscany, Italy, in March 2001 involving 33 experts on nutrition in patients with cystic fibrosis.
450 citations
St James's University Hospital1, Leeds General Infirmary2, Utrecht University3, University of Paris4, University of Toronto5, Necker-Enfants Malades Hospital6, University of Liverpool7, University of St. Gallen8, Medical University of South Carolina9, University Hospital of South Manchester NHS Foundation Trust10, Cork University Hospital11, University of Minnesota12, University of Nottingham13, Goethe University Frankfurt14, Boston Children's Hospital15
TL;DR: A broad overview of the standards expected for newborn screening, diagnosis, preventative treatment of lung disease, nutrition, complications, transplant/end of life care and psychological support in key aspects of CF care, in the context of a fast-moving and dynamic field is given.
439 citations