S
Scott C. Bell
Researcher at University of Queensland
Publications - 345
Citations - 16331
Scott C. Bell is an academic researcher from University of Queensland. The author has contributed to research in topics: Cystic fibrosis & Pseudomonas aeruginosa. The author has an hindex of 58, co-authored 326 publications receiving 13191 citations. Previous affiliations of Scott C. Bell include Translational Research Institute & QIMR Berghofer Medical Research Institute.
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Journal ArticleDOI
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
Bonnie W. Ramsey,Jane C. Davies,N. Gerard McElvaney,Elizabeth Tullis,Scott C. Bell,Pavel Dř evínek,Matthias Griese,Edward F. McKone,Claire E. Wainwright,Michael W. Konstan,Richard B. Moss,Felix Ratjen,Isabelle Sermet-Gaudelus,Steven M. Rowe,Qunming Dong,Sally Rodriguez,Karl Yen,Claudia L. Ordoñez,J. Stuart Elborn +18 more
TL;DR: Ivacaftor was associated with improvements in lung function at 2 weeks that were sustained through 48 weeks and substantial improvements were also observed in the risk of pulmonary exacerbations, patient-reported respiratory symptoms, weight, and concentration of sweat chloride.
Journal ArticleDOI
Genetic mechanisms of critical illness in Covid-19.
Erola Pairo-Castineira,Erola Pairo-Castineira,Sara Clohisey,Lucija Klaric,Andrew D. Bretherick,Konrad Rawlik,Dorota Pasko,Susan P. Walker,Nicholas J. Parkinson,Max Head Fourman,Clark D Russell,James J Furniss,Anne Richmond,E. Gountouna,Nicola Wrobel,David A Harrison,B. Wang,Yang Wu,A. Meynert,Fiona Griffiths,Wilna Oosthuyzen,Athanasios Kousathanas,Loukas Moutsianas,Z. Yang,R. Zhai,Canbin Zheng,Graeme R. Grimes,Rupert Beale,Jonathan E Millar,Barbara Shih,Seán Keating,Marie Zechner,Chris Haley,David J. Porteous,Caroline Hayward,Jian Yang,Julian C. Knight,Charlotte Summers,Manu Shankar-Hari,Manu Shankar-Hari,Paul Klenerman,Lance Turtle,Antonia Ho,S. C. Moore,Charles J. Hinds,P. Horby,Alistair Nichol,Alistair Nichol,Alistair Nichol,David M. Maslove,Lowell Ling,Daniel F. McAuley,Hugh Montgomery,Timothy S. Walsh,Alexandre C. Pereira,Alessandra Renieri,C. Ponting,J. Meikle,P. Finernan,E. Mcmaster,E. Mcmaster,Andy Law,J. K. Baillie,T. Paterson,T. Wackett,Robert C. Armstrong,Robert C. Armstrong,R. Clark,A. Coutts,L. Donnelly,Tamara Gilchrist,K. Hafezi,K. Hafezi,L. Macgillivray,L. Macgillivray,Alan MacLean,Sarah McCafferty,Kirstie Morrice,J. Weaver,C. Boz,C. Boz,A. Golightly,Minghong Ward,H. Mal,H. Szoor-McElhinney,Anthony Brown,Ross Hendry,A. Stenhouse,L. Cullum,D. Law,S. Law,R. Law,Maaike C. Swets,N. Day,F. Taneski,Emma L. Duncan,David Collier,S. Wood,A. Zak,C. Borra,M. Matharu,P. May,Z. Alldis,O. Mitchelmore,R. Bowles,A. Easthope,F. Bibi,I. Lancoma-Malcolm,J. Gurasashvili,J. Pheby,J. Shiel,M. Bolton,Minal Patel,M. Taylor,O. Zongo,P. Ebano,P. Harding,R. Astin-Chamberlain,Y. Choudhury,Anna Cox,D. Kallon,M. Burton,R. Hall,S. Blowes,Z. Prime,J. Biddle,O. Prysyazhna,T. Newman,C. Tierney,J. Kassam,Marlies Ostermann,S. Campos,A. Bociek,R. Lim,N. Grau,T. O. Jones,C. Whitton,M. Marotti,Gill Arbane,S. Bonner,K. Hugill,J. Reid,Ingeborg Welters,V. Waugh,Katherine Williams,D. Shaw,J. F. Roman,M. L. Martinez,Elizabeth M. Johnson,A. Waite,B. Johnston,D. Hamilton,S. Mulla,Mark J. W. McPhail,John A. S. Smith,L. Barclay,D. Hope,Corrienne McCulloch,L. McQuillan,S. Clark,J. Singleton,K. Priestley,N. Rea,M. Callaghan,R. Campbell,G. Andrew,L. Marshall,Stuart McKechnie,P. Hutton,A. Bashyal,N. Davidson,P. Polgarova,K. Stroud,N. Pathan,K. Elston,Sutapa Agrawal,Ceri Battle,L. Newey,Tim Rees,R. Harford,E. Brinkworth,Martin S. Williams,C. Murphy,I. M. S. White,M. Croft,N. Bandla,M. Gellamucho,J. Tomlinson,H. Turner,Michael Davies,A. Quinn,I. Hussain,Christopher C. Thompson,H. Parker,R. Bradley,R. Griffiths,J. Scriven,A. Nilsson,Matthew G.D. Bates,J. Dasgin,Janusz Gill,Alex Puxty,S. Cathcart,D. Salutous,L. Turner,K. Duffy,K. Puxty,Anna Maria Joseph,R. Herdman-Grant,R. Simms,A. Swain,A. Naranjo,R. Crowe,K. Sollesta,A. Loveridge,D. Baptista,E. Morino,M. Davey,D. Golden,J. Jones,J. Moreno Cuesta,A. Haldeos,D. Bakthavatsalam,Royce P Vincent,M. Elhassan,K. Xavier,Anand K. Ganesan,D. Purohit,M. Abdelrazik,J.M. Morgan,L. Akeroyd,S. Bano,T. Lawton,D. Warren,M. Bromley,K. Sellick,L. Gurr,B. Wilkinson,V. Nagarajan,P. Szedlak,Jason Cupitt,E. Stoddard,L. Benham,S. Preston,Shondipon Laha,N. Slawson,Z. Bradshaw,Jamie Brown,M. Caswell,S. Melling,P. Bamford,M. Faulkner,K. Cawley,H. Jeffrey,E. London,H. Sainsbury,I. Nagra,F. Nasir,C. Dunmore,R. L. Jones,A. Abraheem,M. Al-Moasseb,R. Girach,G. Padden,Josephine M. Egan,C. Brantwood,P. Alexander,J. Bradley-Potts,Susan Allen,Timothy Felton,S. Manna,S. Farnell-Ward,S. Leaver,J. Queiroz,E. Maccacari,D. Dawson,C. C. Delgado,R. P. Saluzzio,O. Ezeobu,L. Ding,C. Sicat,R. Kanu,G. Durrant,J. Texeira,Abby Harrison,T. Samakomva,H. Willis,B. Hopkins,L. Thrasyvoulou,M. Jackson,A. Zaki,C. Tibke,Suzanne Bennett,W. Woodyatt,A. Kent,E. Goodwin,C. Brandwood,Lee B. Smith,Kevin Rooney,Neil C. Thomson,N. Rodden,Ellen C Hughes,D. McGlynn,C. Clark,P. Clark,Laurent Abel,R. Sundaram,L. Gemmell,M. Brett,J. Hornsby,P. MacGoey,R. Price,B. Digby,P. O'Neil,P. McConnell,Paul Henderson,Seton J Henderson,M. Sim,S. Kennedy-Hay,C. McParland,L. Rooney,N. Baxter,D. Pogson,S. Rose,Z. Daly,L. Brimfield,Mandeep Phull,M. Hussain,T. Pogreban,L. Rosaroso,E. Salciute,L. Grauslyte,David Brealey,Eamon P. Raith,N. MacCallum,G. Bercades,I. Hass,D. Smyth,A. Reyes,G. Martir,I. D. Clement,K. Webster,C. Hays,A. Gulati,Luke Hodgson,M. Margarson,Refujia Gomez,Y. Baird,Y. Thirlwall,L. Folkes,A. Butler,E. Meadows,Shona C Moore,D. Raynard,Helen C. Fox,L. Riddles,K. King,S. Kimber,G. Hobden,Anne Marie McCarthy,V. Cannons,I. Balagosa,I. Chadbourn,A. Gardner,D. Horner,D. McLaughlanv,B. Charles,N. Proudfoot,T. Marsden,L. McMorrow,B. Blackledge,J. Pendlebury,Alison G. Harvey,E. Apetri,C. Basikolo,L. Catlow,R. Doonan,K. Knowles,S. Lee,David A. Lomas,C. Lyons,Joseph Perez,M. Poulaka,M. Slaughter,K. Slevin,V. Thomas,David W. Walker,Jennifer R. Harris,A. Drummond,R. Tully,J. Dearden,J. Philbin,S. Munt,C. Rishton,G. O'Connor,M. Mulcahy,E. Dobson,J. Cuttler,M. Edward,Jill M. Norris,K. Hanson,Alexis Poole,Alistair Rose,B. Sloan,S. Buckley,H. Brooke,E. Smithson,R. Charlesworth,R. Sandhu,M. Thirumaran,V. Wagstaff,J. C. Suarez,Agilan Kaliappan,M. Vertue,Andrew G. Nicholson,J. Riches,A. Solesbury,L. Kittridge,M. Forsey,G. Maloney,John B. Cole,R. Davies,H. Hill,E L Thomas,A. Williams,D. Duffin,B. Player,Jayachandran Radhakrishnan,Spencer B. Gibson,A. Lyle,F. McNeela,Brijesh V. Patel,M. Gummadi,G. Sloane,N. Dormand,S. Salmi,Z. Farzad,D. Cristiano,K. Liyanage,V. Thwaites,M. Varghese,M. Meredith,Gordon B. Mills,J. Willson,K. Harrington,B. Lenagh,K. Cawthron,S. Masuko,A. Raithatha,K. Bauchmuller,M. Wiles,N. Ahmad,Jack Barker,Y. Jackson,F. Kibutu,Sara W. Bird,G. Watson,Javier Martin,E. Bevan,C. W. Brown,D. Trodd,K. English,Graeme I. Bell,L. Wilcox,A. Katary,S. Gopal,V. Lake,N. Harris,S. Metherell,Elizabeth J. Radford,F. Moore,H. Bancroft,J. Daglish,M. Sangombe,M. Carmody,Johanna Rhodes,M. Bellamy,Atul Garg,A. Kuravi,E. Virgilio,P. Ranga,Javed Butler,L. Botfield,C. Dexter,Jason Fletcher,P. Shanmugasundaram,G. Hambrook,I. Burn,K. Manso,D. Thornton,J. Tebbutt,R. Penn,J. Hulme,Sabah N. A. Hussain,Z. Maqsood,Sarah B. Joseph,J. Colley,A. Hayes,C. Ahmed,R. Haq,S. Clamp,Rakesh Kumar,M. Purewal,B. Baines,M. Frise,N. Jacques,H. Coles,J. Caterson,S. G. Rai,M. Brunton,E. Tilney,L. Keating,Andrew Walden,David Antcliffe,Stephen J. Brett,Anthony C. Gordon,M. Templeton,Rocio Rojo,D. Banach,S. S. Arias,Z. Fernandez,P. Coghlan,D. Williams,Catherine Jardine,J. Bewley,Katie Sweet,L. Grimmer,Randall S. Johnson,Z. Garland,B. Gumbrill,C. Phillips,L. Ortiz-Ruiz de Gordoa,E. Peasgood,Ascanio Tridente,K. Shuker,S. Greer,C. Lynch,C. Pothecary,L. Roche,B. Deacon,K. Turner,Jai Rup Singh,G. S. Howe,P. Paul,Michael Gill,I. Wynter,V. Ratnam,S. Shelton,Jay Naisbitt,J. Melville,R. Baruah,Siouxzy Morrison,A. McGregor,V. Parris,M. Mpelembue,S. Srikaran,C. Dennis,A. Sukha,M. Verlander,K. Holding,K. Riches,C. Downes,C. Swan,A. Rostron,Ajit Roy,L. Woods,S. Cornell,F. Wakinshaw,Ben Creagh-Brown,H. Blackman,A. Salberg,E. N. Smith,S. Donlon,S. Mtuwa,N. Michalak-Glinska,S. Stone,C. Beazley,V. Pristopan,N. Nikitas,L. Lankester,Christine A. Wells,A. S. Raj,Katherine Fletcher,R. Khade,G. Tsinaslanidis,Michael MacMahon,Stephen J. Fowler,T. Coventry,Richard B. Stewart,L. Wren,E. Mwaura,L. Mew,D. Scaletta,Frances M K Williams,K. Inweregbu,N. Lancaster,Matthew Cunningham,A. Daniels,L. Harrison,S. Hope,S Jones,A. Crew,G. Wray,John N. S. Matthews,R. Crawley,J. Carter,I. Birkinshaw,J. Ingham,Z. Scott,H. Pearson,K. Howard,R. Joy,S. Roche,M. Clark,S. Purvis,Alanna C. Morrison,David P. Strachan,S. Clements,K. Black,Chetan Parmar,A. Altabaibeh,Kenneth J. Simpson,L. Mostoles,K. Gilbert,L. Ma,A. Alvaro,Mark G. Thomas,B. Faulkner,R. Worner,Kate Hayes,E. Gendall,H. Blakemore,B. Borislavova,E. Goff,Alan Vuylsteke,L. Mwaura,J. Zamikula,L Garner,A. Mitchell,S. Mepham,L. Cagova,A. Fofano,H. Holcombe,K. Praman,Tamas Szakmany,A. E. Heron,S. Cherian,S. Cutler,A. Roynon-Reed,G. Randell,K. Convery,K. Stammers,D. Fottrell-Gould,L. Hudig,J. Keshet-Price,Mark J. Peters,L. O'Neill,Swapan K. Ray,H. Belfield,T. McHugh,Graeme Jones,O. Akinkugbe,A. Tomas,E. Abaleke,E. Beech,H. Meghari,S. Yussuf,A. Bamford,B. Hairsine,E. Dooks,F. Farquhar,S. Packham,H. Bates,Lawrence Armstrong,C. Kaye,A. Allan,J. Medhora,J. Liew,A. Botello,F. Anderson,Rebecca Cusack,H. Golding,K. Prager,Thomas N. Williams,S. Leggett,K. Golder,M. Male,O. Jones,K. Criste,M. Marani,V. Anumakonda,V. Amin,K. Karthik,R. Kausar,E. Anastasescu,K. Reid,Mari Smith,Anil Hormis,Rosie M. Walker,T. Duncan,A. Uriel,Andrew Ustianowski,H. T-Michael,M. Bruce,K. Connolly,Kenneth Smith,Roland Partridge,Darren K. Griffin,M. Mupudzi,N. Muchenje,Dori-Ann Martin,H. Filipe,C. Eastgate,C. Jackson,Andrew Gratrix,L. Foster,Victoria Martinson,E. Stones,C. Abernathy,P. Parkinson,A. Reed,C. Prendergast,Peter Rogers,M. Woodruff,R. Shokkar,S Kaul,A. Barron,C. Collins,S. Beavis,A. Whileman,K. Dale,J. Hawes,K. Pritchard,R. Gascoyne,L. Stevenson,R. Jha,L. Lim,V. Krishnamurthy,Roy Parker,I. Turner-Bone,L. Wilding,A. Reddy,S. Whiteley,E. Wilby,C. Howcroft,A. Aspinwall,Sue Charlton,B. Ogg,Donna J. Menzies,Richard Pugh,E. Allan,R. Lean,F. Davies,J. Easton,X. Qiu,Shriya B. Kumar,K. Darlington,G. Houston,P. O'Brien,T. Geary,Jay Allan,A. Meikle,Grant L. Hughes,M. Balasubramaniam,S. Latham,E. McKenna,R. Flanagan,S. Sathe,Emma L. Davies,M. Chablani,A. Kirkby,K. Netherton,S. Archer,Bryan Yates,C. Ashbrook-Raby,Sarah Cole,M. Casey,L. Cabrelli,Stephen Chapman,A. Hutcheon,C. Whyte,C. Almaden-Boyle,Natalie Pattison,Claudina Cruz,A. Vochin,H. Kent,Adri A. M. Thomas,S. Murdoch,B. David,M. Penacerrada,G. Lubimbi,V. Bastion,R. Wulandari,Roberto Lorusso,J. Valentine,D. Clarke,A. Serrano-Ruiz,S. Hierons,C. Eckbad,L. Ramos,C. Demetriou,S. Mitchard,K. White,Nicholas J. White,Steven J. Pitts,D. Branney,J. Frankham,M. Watters,H. Langton,Rachel Prout,V. Page,T. Varghes,A. Cowton,A. Kay,K. Potts,M. Birt,Matthew Peter Kent,A. Wilkinson,E. B. Jude,V. Turner,H. Savill,J. McCormick,M. Coulding,S. Siddiqui,O. Mercer,H. Rehman,D. Potla,N. Capps,David S. Donaldson,H. Button,Terry Martin,K. Hard,A. Agasou,L. Tonks,T. Arden,Patricia A. Boyle,M. Carnahan,J. Strickley,Christopher M. Adams,D. Childs,R. Rikunenko,M. Leigh,M. Breekes,R. Wilcox,A. Bowes,H. Tiveran,F. Hurford,J. Summers,Austin Carter,Y. Hussain,L. Ting,A. Javaid,N. Motherwell,H. Moore,H. Millward,S. Jose,N. Schunki,A. Noakes,C. Clulow,G. Sadera,Reni Jacob,Chris Jones,M. Blunt,Z. Coton,H. Curgenven,S. M. Ally,K. Beaumont,M. Elsaadany,K. Fernandes,I. Ali Mohamed Ali,H. Rangarajan,V. Sarathy,S. Selvanayagam,D. Vedage,M. White,N. Truman,Srikanth Chukkambotla,S. Keith,J. Cockerill-Taylor,J. Ryan-Smith,R. Bolton,P. Springle,J. Dykes,Jo Thomas,Muzamil Majid Khan,M. T. Hijazi,E. Massey,G. Croston,Henrik Reschreiter,Julie Camsooksai,S. Patch,S. Jenkins,C. Humphrey,B. Wadams,M. Msiska,O. Adanini,B. Attwood,P. Parsons,Kate Tatham,S. Jhanji,E. Black,A. Dela Rosa,R. Howle,B. Thomas,T. Bemand,R. Raobaikady,R. Saha,Nikki Staines,A. Daniel,J. Finn,J. Hutter,P. Doble,C. Shovelton,C. Pawley,T. Kannan,Michael Hill,E. Combes,S. Monnery,T. Joefield,M. Popescu,M. Thankachen,M. Oblak,Jeff Little,S. McIvor,A. Brady,H. Whittle,H. Prady,R. Chan,A. Ahmed,Andrew D. Morris,C. Gibson,E. Gordon,S. Keenan,H. Quinn,S. Benyon,S. Marriott,L. Zitter,L. Park,K. Baines,M. Lyons,M. Holland,N. Keenan,M. Young,S. Garrioch,J. Dawson,M. Tolson,B. Scholefield,R. Bi,Neil Richardson,N. Schumacher,T. Cosier,G. Millen,A. Higham,S. Turki,L. Allen,N. Crisp,T. Hazleton,A. Knight,J. Deery,C. Price,S. Turney,S. Tilbey,E. Beranova,Derek W. Wright,L. George,S. Twiss,S. Wadd,K. Postlethwaite,P. Gondo,B. Masunda,A. Kayani,B. Hadebe,J. Whiteside,N. Clarke,Phil Donnison,F. Trim,I. Leadbitter,D. Butcher,S. O'Sullivan,B. Purewal,Scott C. Bell,V. Rivers,R. O'Leary,J. Birch,E. Collins,Stephen K. Anderson,K. Hammerton,E. Andrews,K. Burns,I. Edmond,A. Todd,J. Donnachie,P. Turner,L. Prentice,L. Symon,N. Runciman,F. Auld,M. Halkes,P. Mercer,L. Thornton,G. Debreceni,J. Wilkins,V. Crickmore,G. Subramanian,Robert Marshall,C. Jennings,M. Latif,L. Bunni,M. Spivey,S. Bean,K. Burt,Vanessa Linnett,J. Ritzema,A. Sanderson,W. McCormick,M. Bokhari,R. Kapoor,D. Loader,A. Ayers,W. Harrison,J. North,Z. Belagodu,R. Paramsothy,O. Olufuwa,A. Gherman,B. Fuller,C. Stuart,O. Kelsall,Carrie A. Davis,L. Wild,Henry Wood,Jessica Thrush,A. Durie,K. Austin,K. Archer,P. Anderson,C. Vigurs,C. Thorpe,E. Knights,N. Boyle,Alkes L. Price,A. Kubisz-Pudelko,D. Wood,Amy Lewis,S. Board,L. Pippard,John R. B. Perry,K. Beesley,A. Rattray,E. Lee,L. Lennon,K. Douglas,D. Bell,R. Boyle,L. Glass,M. Nauman Akhtar,K. Dent,D. Potoczna,S. Pearson,E. Horsley,S. Spencer,D. Mullan,D. Skinner,J. Gaylard,R. Barber,C. Hewitt,A. Hilldrith,S. Shepardson,M. Wills,K. Jackson-Lawrence,A. Gupta,E. Timlick,C. Gorman,Igor Otahal,A. Gales,S. Coetzee,Christian Sell,M. Raj,M. Peiu,S. Quaid,E. Watson,Katherine S. Elliott,J. Mallinson,B. Chandler,A. Turnbull,C. Finch,C. Holl,J.A. Cooper,Anthony Evans,W. Khaliq,Andrea M. Collins,E. T. Gude,N. Love,L. van Koutrik,John A. Hunt,D. Kaye,Eva Fisher,A. Brayne,V. Tuckey,P. Jackson,J. Parkin,A. Tariq,Henry Houlden,A. Tucci,John Hardy,E. Moncur,J. Highgate,A. Cowley,A. Mitra,R. Stead,T. Behan,C. Burnett,M. Newton,E. Heeney,R. Pollard,J. Hatton,Amita Patel,Vidya Kasipandian,S. Allibone,R. M. Genetu,L. O'Brien,Z. Omar,E. Perkins,Kevin A. Davies,D. Tetla,B. Shelley,V. Irvine,Samantha J. Williams,Patricia Williams,J. Goodsell,R. Tutton,L. Bough,B. Winter-Goodwin,R. Kitson,J. Pinnell,Anthony J. Wilson,T. Nortcliffe,T. Wood,M. Home,K. Holdroyd,Matthew R. Robinson,R. Shaw,J. Greig,M. Brady,A. Haigh,L. Matupe,M. Usher,S. Mellor,S. Dale,L. Gledhill,L. Shaw,G. Turner,Donna Kelly,B. Anwar,Heather L. Riley,H. Sturgeon,A. Ali,L. Thomis,D. Melia,A. Dance,SE Humphreys,I. Frost,V. Gopal,Jo Godden,A. Holden,S. Swann,Tony Smith,M. Clapham,U. Poultney,R. Harper,P. Rice,R. Reece-Anthony,B. Gurung,S. Moultrie,M. Odam,Andreas Mayer,A. Bellini,A. Pickard,J. Bryant,N. Roe,J. Sowter,K. Lang,Jenny C. Taylor,P. Barry,Maria Hobrok,H. Tench,R. Wolf-Roberts,H. McGuinness,R. Loosley,Daniel B Hawcutt,L. Rad,L. O'Malley,P. Saunderson,G. Seddon,Tim J. Anderson,N. Rogers,J. Ruddy,M. Harkins,C. Beith,A. McAlpine,L. Ferguson,Paul Grant,S. MacFadyen,M. McLaughlin,T. Baird,S. Rundell,B. Welsh,R. Hamill,F. Fisher,J. Gregory,Campbell A,S. Smuts,J Kenneth Baillie,J Kenneth Baillie,Gail Carson,Beatrice Alex,B. Bach,Wendy S. Barclay,Debby Bogaert,Meera Chand,Graham S Cooke,Annemarie B Docherty,Jake Dunning,A. da Silva Filipe,Tom Fletcher,Christopher A Green,Ewen M Harrison,Julian A. Hiscox,Ho A. Y. W.,Peter Horby,Samreen Ijaz,S. Khoo,W. S. Lim,Alexander J. Mentzer,Laura Merson,Alison M. Meynert,Mahdad Noursadeghi,Massimo Palmarini,William A. Paxton,Georgios Pollakis,Nicholas Price,Andrew Rambaut,David Robertson,Vanessa Sancho-Shimizu,Janet T Scott,T I de Silva,Louise Sigfrid,Tom Solomon,Shiranee Sriskandan,David I. Stuart,R.S. Tedder,E. Thomson,Alfred A.R. Thompson,Ryan S Thwaites,L Turtle,Maria Zambon,Hayley Hardwick,Chloe Donohue,Ronan A Lyons,Lisa Norman,Riinu Pius,Thomas M Drake,Cameron J Fairfield,Stephen R Knight,Kenneth A. McLean,Derek Murphy,C. A. Shaw,Jo Dalton,Michelle Girvan,Egle Saviciute,Stuart K. Roberts,Janet Harrison,Laura Marsh,Marie Connor,Sophie Halpin,Carrol Gamble,Gary Leeming,Murray Wham,William Greenhalf,V. Shaw,Sarah D. McDonald,Andrea Ganna,Patrick Sulem,D A van Heel,M. Cordioli,Gardar Sveinbjornsson,M. E. K. Niemi,Janie F. Shelton,A. J. Shastri,C. Ye,C. H. Weldon,T. Filshtein-Sonmez,D. Coker,A. Symons,J. Esparza-Gordillo,Stella Aslibekyan,Adam Auton,J. E. Krieger,E. Marques,C. E. Jannes,Francesca Mari,S. Daga,Margherita Baldassarri,Elisa Benetti,Simone Furini,Chiara Fallerini,Francesca Fava,Floriana Valentino,G. Doddato,Annarita Giliberti,Rossella Tita,Sara Amitrano,Mirella Bruttini,S. Croci,I. Meloni,A. M. Pinto,E. Frullanti,Maria Antonietta Mencarelli,C. L. Rizzo,Francesca Montagnani,L. Di Sarno,A. Tommasi,Marta Palmieri,Arianna Emiliozzi,M. Fabbiani,Barbara Rossetti,Giacomo Zanelli,Elena Bargagli,Laura Bergantini,Miriana d'Alessandro,Paolo Cameli,D. Bennet,Federico Anedda,Simona Marcantonio,Sabino Scolletta,Federico Franchi,Maria Antonietta Mazzei,S. Guerrini,Edoardo Conticini,Luca Cantarini,Bruno Frediani,D. Tacconi,C. Spertilli,M. Feri,Abele Donati,R. Scala,L. Guidelli,G. Spargi,M. Corridi,C. Nencioni,L. Croci,G. P. Caldarelli,M. Spagnesi,P. Piacentini,M. Bandini,E. Desanctis,S. Cappelli,A. Canaccini,A. Verzuri,V. Anemoli,A. Ognibene,M. Vaghi,A d'Arminio Monforte,Esther Merlini,M. U. Mondelli,S. Mantovani,S. Ludovisi,Massimo Girardis,S. Venturelli,M. Sita,Andrea Cossarizza,A. Antinori,Alessandra Vergori,Stefano Rusconi,M. Siano,A. Gabrieli,Agostino Riva,Daniela Francisci,Elisabetta Schiaroli,P. G. Scotton,F. Andretta,S. Panese,R. Scaggiante,F. Gatti,S. G. Parisi,Francesco Castelli,M. E. Quiros-Roldan,P. Magro,Isabella Zanella,M. Della Monica,Carmelo Piscopo,Mario Capasso,Roberta Russo,Immacolata Andolfo,Achille Iolascon,G. Fiorentino,M. Carella,Marco Castori,Giuseppe Merla,Filippo Aucella,P. Raggi,C. Marciano,R. Perna,Matteo Bassetti,A. Di Biagio,M. Sanguinetti,L. Masucci,Serafina Valente,Marco Mandalà,A. Giorli,L. Salerni,P. Zucchi,P. Parravicini,E. Menatti,S. Baratti,T. Trotta,F. Giannattasio,G. Coiro,F. Lena,D. A. Coviello,Cristina Mussini,G. Bosio,E. Martinelli,Sandro Mancarella,L. Tavecchia,L. Crotti,N. Picchiotti,M. Gori,C. Gabbi,M. Sanarico,S. Ceri,P. Pinoli,F. Raimondi,F. Biscarini,A. Stella,Xia Shen,Xia Shen,Chris P. Ponting,Angie Fawkes,Albert Tenesa,Albert Tenesa,Mark J. Caulfield,Richard H Scott,K Rowan,Lee Murphy,Peter J. M. Openshaw,Peter J. M. Openshaw,Malcolm G Semple,Veronique Vitart,James F. Wilson +1449 more
TL;DR: The GenOMICC (Genetics Of Mortality In Critical Care) genome-wide association study in 2244 critically ill Covid-19 patients from 208 UK intensive care units is reported, finding evidence in support of a causal link from low expression of IFNAR2, and high expression of TYK2, to life-threatening disease.
Journal ArticleDOI
Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: A randomised trial
TL;DR: AZM in adults with CF significantly improved QOL, reduced CRP levels and the number of respiratory exacerbations, and reduced the rate of decline in lung function, suggesting long term AZM may have a significant impact on morbidity and mortality in patients with CF.
Journal ArticleDOI
ECFS best practice guidelines: the 2018 revision
Carlo Castellani,Alistair J.A. Duff,Alistair J.A. Duff,Scott C. Bell,Harry G.M. Heijerman,Anne Munck,Felix Ratjen,Isabelle Sermet-Gaudelus,Kevin W Southern,Jürg Barben,Patrick A. Flume,Pavla Hodková,Nataliya Kashirskaya,Maya Kirszenbaum,Sue Madge,H. Oxley,Barry J. Plant,Sarah Jane Schwarzenberg,Alan R. Smyth,Giovanni Taccetti,Thomas O. F. Wagner,Susan P. Wolfe,Pavel Drevinek +22 more
TL;DR: A broad overview of the standards expected for newborn screening, diagnosis, preventative treatment of lung disease, nutrition, complications, transplant/end of life care and psychological support in key aspects of CF care, in the context of a fast-moving and dynamic field is given.
Journal ArticleDOI
Control of Confounding and Reporting of Results in Causal Inference Studies. Guidance for Authors from Editors of Respiratory, Sleep, and Critical Care Journals
David J. Lederer,Scott C. Bell,Richard D. Branson,James D. Chalmers,Rachel Marshall,David M. Maslove,David Ost,Naresh M. Punjabi,Michael Schatz,Alan R. Smyth,Paul W. Stewart,Samy Suissa,Alex A. Adjei,Cezmi A. Akdis,Elie Azoulay,Jan Bakker,Jan Bakker,Jan Bakker,Zuhair K. Ballas,Philip G. Bardin,Esther Barreiro,Rinaldo Bellomo,Jonathan A. Bernstein,Vito Brusasco,Timothy G. Buchman,Sudhansu Chokroverty,Nancy A. Collop,James D. Crapo,Dominic A. Fitzgerald,Lauren Hale,Nicholas Hart,Felix J.F. Herth,Theodore J. Iwashyna,Gisli Jenkins,Martin Kolb,Guy B. Marks,Peter J. Mazzone,J. Randall Moorman,Thomas M. Murphy,Terry L. Noah,Paul N. Reynolds,Dieter Riemann,Richard Russell,Richard Russell,Aziz Sheikh,Giovanni Sotgiu,Erik R. Swenson,Rhonda D. Szczesniak,Rhonda D. Szczesniak,Ronald Szymusiak,Jean-Louis Teboul,Jean Louis Vincent +51 more
TL;DR: Control of Confounding and Reporting of Results in Causal Inference Studies Guidance for Authors from Editors of Respiratory, Sleep, and Critical Care Journals is published.