Journal ArticleDOI
Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome: fevers, myalgia, arthralgia, auricular chondritis, and erythema nodosum.
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This article is published in The Lancet.The article was published on 2021-08-14. It has received 17 citations till now. The article focuses on the topics: Erythema nodosum & Chondritis.read more
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'VEXAS Syndrome (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) for the Dermatologist'.
David Sterling,M H Duncan,M. Philippidou,Jonathan R. Salisbury,Austin G. Kulasekararaj,Tanya N Basu +5 more
TL;DR: A review of the dermatological features of VEXAS syndrome can be found in this article , where a wide range of skin presentations are reported, including Sweet-like urticated and tender erythematous nodules, cartilaginous involvement with chondritis, cutaneous vasculitis, and periorbital angiodema.
Journal ArticleDOI
A case of VEXAS syndrome associated with EBV-associated hemophagocytic lymphohistiocytosis
TL;DR: In this article , the first case of EBV-associated hemophagocytic lymphohistiocytosis (HLH) was described in a patient diagnosed with VEXAS syndrome.
Journal ArticleDOI
A case of VEXAS syndrome associated with EBV-associated hemophagocytic lymphohistiocytosis
Roy L. Kao,Audrey A. Jacobsen,Charles J. Billington,Sophia Yohe,Amy Beckman,Gregory M. Vercellotti,David R. Pearson +6 more
TL;DR: In this article, the first case of EBV-associated hemophagocytic lymphohistiocytosis (HLH) was described in a patient diagnosed with VEXAS syndrome.
Journal ArticleDOI
Innovations in genomics for undiagnosed diseases: vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome
TL;DR: Autoinflammatory syndromes should be considered for patients with fever of unknown origin for whom extensive investigation for infection, malignant disease, hemo-phagocytic syndrome and other causes of fever and systemic inflammation have been excluded.
Journal ArticleDOI
Vasculitis associated with VEXAS syndrome: A literature review
TL;DR: Vasculitis can be an initial manifestation of VEXAS syndrome, a novel autoinflammatory syndrome that connects seemingly unrelated conditions: inflammatory syndromes and hematologic disorders (myelodysplastic syndrome or multiple myeloma).