S
Sibilla Molon
Researcher at University of Padua
Publications - 5
Citations - 473
Sibilla Molon is an academic researcher from University of Padua. The author has contributed to research in topics: Skeletal muscle & Collagen VI. The author has an hindex of 4, co-authored 4 publications receiving 396 citations.
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Journal ArticleDOI
Collagen VI regulates satellite cell self-renewal and muscle regeneration
Anna Urciuolo,Marco Quarta,Valeria Morbidoni,Francesca Gattazzo,Sibilla Molon,Paolo Grumati,Francesca Montemurro,Francesco Tedesco,Bert Blaauw,Giulio Cossu,Giovanni Vozzi,Thomas A. Rando,Paolo Bonaldo +12 more
TL;DR: It is shown that the extracellular matrix protein collagen VI is a key component of the satellite cell niche and establishes a critical role for an extracllular matrix molecule in satellite cell self-renewal and open new venues for therapies of collagen VI-related muscle diseases.
Journal ArticleDOI
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of SBMA muscle modified by high-fat diet.
Anna Rocchi,Carmelo Milioto,Carmelo Milioto,Sara Parodi,Sara Parodi,Andrea Armirotti,Doriana Borgia,Matteo Pellegrini,Anna Urciuolo,Sibilla Molon,Valeria Morbidoni,Manuela Marabita,Vanina Romanello,Pamela Gatto,Bert Blaauw,Paolo Bonaldo,Fabio Sambataro,Diane M. Robins,Andrew P. Lieberman,Gianni Sorarù,Lodovica Vergani,Marco Sandri,Maria Pennuto,Maria Pennuto +23 more
TL;DR: It is shown that glycolytic muscles were more severely affected than oxidative muscles in SBMA knock-in mice, and an HFD regime is highlighted as a promising approach to support SBMA patients.
Journal ArticleDOI
Cyclosporin A Promotes in vivo Myogenic Response in Collagen VI-Deficient Myopathic Mice.
Francesca Gattazzo,Francesca Gattazzo,Sibilla Molon,Valeria Morbidoni,Paola Braghetta,Bert Blaauw,Anna Urciuolo,Paolo Bonaldo +7 more
TL;DR: It is shown that under appropriate administration, regimens CsA is able to stimulate myogenesis in Col6a1−/− mice by significantly increasing the number of myogenin (MyoG)-positive cells and of regenerating myofibers at the early stages of muscle regeneration.
Journal ArticleDOI
Collagen VI Null Mice as a Model for Early Onset Muscle Decline in Aging.
Daniele Capitanio,Manuela Moriggi,Sara De Palma,Dario Bizzotto,Sibilla Molon,Enrica Torretta,Chiara Fania,Paolo Bonaldo,Cecilia Gelfi,Paola Braghetta +9 more
TL;DR: Comparison of the proteomic features and the molecular analysis of metabolic and autophagic pathways in adult and aged Col6a1−/− diaphragm indicated that the effects of aging, culminating in lipotoxicity and Autophagic impairment, were already present at 6 months of age.
Journal ArticleDOI
Collagen VI promotes recovery from colitis by inducing lymphangiogenesis and drainage of inflammatory cells
Sibilla Molon,Paola Brun,Melania Scarpa,Dario Bizzotto,Gaia Zuccolotto,Marco Scarpa,Matteo Fassan,Imerio Angriman,Antonio Rosato,Paola Braghetta,Ignazio Castagliuolo,Paolo Bonaldo +11 more
TL;DR: This paper investigated the role of a major ECM protein, collagen VI (ColVI), in gut homeostasis and elucidated the impact of its deregulation on the pathophysiology of IBD.