Journal ArticleDOI
A new form of heredo-familial spinocerebellar degeneration with slow eye movements (nine families)
N. H. Wadia,R. K. Swami +1 more
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This article is published in Brain.The article was published on 1971-01-01. It has received 166 citations till now. The article focuses on the topics: Spinocerebellar Degenerations.read more
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Cerebellar Degenerations: Clinical Neurobiology
TL;DR: The Cerebellar Cortex and the Dentate Nucleus in Hereditary Ataxias A. Plaitakis and his colleagues propose a new model of Neuro-Immune Degeneration, based on a model of Human Ataxia in Humans, which is compatible with the model used in Europe.
Journal ArticleDOI
Saccadic premotor neurons in the brainstem: functional neuroanatomy and clinical implications
TL;DR: The localization of some premotor saccadic neurons in human brain and their neurochemistry are described, based on monkey data.
Journal ArticleDOI
Supranuclear disorders of eye movement.
D G Milder,Francis A. Billson +1 more
TL;DR: An algorithm for the analysis of supranuclear eye movement disorders is presented and may be divided into nystagmus, other ocular oscillations, saccadic dysfunction, smooth pursuit dysfunction, gaze palsy, tonic deviation, and vergence disability.
Journal ArticleDOI
Alterations of ocular motility in cerebellar pathology. An electro-oculographic study.
TL;DR: A tendency to produce saccades slower than normal was noted in patients affected by olivopontocerebellar atrophy, and the clinical and pathophysiological significance of this finding is discussed with particular reference to Wadia-Swaami hereditary ataxia.
Journal ArticleDOI
Saccade velocity as a surrogate disease marker in spinocerebellar ataxia type 2.
Carola Seifried,Luis Velázquez-Pérez,N. Santos-Falcón,M. Abele,Ulf Ziemann,L. Almaguer,E Martínez-Góngora,Sánchez-Cruz G,Nalia Canales,Ruth Pérez-González,Mercedes Velázquez-Manresa,B. Viebahn,S Stuckrad-Barre,Thomas Klockgether,Michael Fetter,Georg Auburger +15 more
TL;DR: Spinocerebellar ataxia type 2 patients and controls maximal saccade velocity (MSV) is strongly decreased in SCA2 patients and is influenced mostly by polyglutamine size.
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