Journal ArticleDOI
An asthmatic adolescent with a rash and eosinophilia.
Muhammad Waseem,Emma Laureta +1 more
TLDR
A young asthmatic adolescent who presented with vasculitis, eosinophilia, and peripheral neuropathy is reported, which may increase the morbidity from the complications of Vasculitis.Abstract:
Children frequently visit emergency departments with asthma exacerbations. Many of these asthmatic children may have fever and/or pneumonia, but when associated with eosinophilia or evidence of vasculitis, other diagnoses should be considered. Churg-Strauss syndrome is a rare form of systemic vasculitis, which usually occurs in patients with asthma in association with eosinophilia. The diagnosis of Churg-Strauss syndrome can be difficult because this syndrome may arise at first as a common association between asthma and allergic rhinitis. A delay in diagnosis and treatment may increase the morbidity from the complications of vasculitis. We report a young asthmatic adolescent who presented with vasculitis, eosinophilia, and peripheral neuropathy.read more
Citations
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Eosinophilic granulomatosis with polyangiitis in children: Data from the French RespiRare® cohort.
Agnès Fina,Jean-Christophe Dubus,Antoine Tran,Jocelyne Derelle,Philippe Reix,Michael Fayon,Laure Couderc,Marie-Dominique Donnou,Anne Pagnier,Sylvain Blanchon,Nathalie Faure,Laurent Mely,M. Albertini,Jacques de Blic,Lisa Giovannini-Chami +14 more
TL;DR: The characteristics of pediatric cases of eosinophilic granulomatosis with polyangiitis (EGPA), a systemic necrotizing vasculitis rarely diagnosed in children, are described and compared with adult cases included in the French Vasculitis Study Group cohort.
Journal ArticleDOI
Clinical presentation of Churg–Strauss syndrome in children: A 12-year-old-boy with ANCA-negative Churg–Strauss syndrome
Femke G.E.M. Razenberg,Jan Heynens,Geeuwke Jan de Vries,Liesbeth Duijts,Johan C. de Jongste,Jacques de Blic,Philippe P.R. Rosias +6 more
TL;DR: A 12-year-old boy with asthma and deterioration of his general condition, who was eventually diagnosed with an ANCA-negative Churg–Strauss syndrome is reported on.
Journal ArticleDOI
Cutaneous manifestations of childhood Eosinophilic Granulomatosis with Polyangiitis (cEGPA): A case-based review.
TL;DR: This study seeks to better define the clinical presentation and histopathology of cutaneous manifestations in childhood eosinophilic granulomatosis with polyangiitis (cEGPA).
References
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Journal ArticleDOI
The American College of Rheumatology 1990 criteria for the classification of churg‐strauss syndrome (allergic granulomatosis and angiitis)
Alfonse T. Masi,Alfonse T. Masi,Gene G. Hunder,Gene G. Hunder,J. T. Lie,J. T. Lie,Beat A. Michel,Daniel A. Bloch,Daniel A. Bloch,William P. Arend,William P. Arend,Leonard H. Calabrese,Leonard H. Calabrese,Steven M. Edworthy,Steven M. Edworthy,Anthony S. Fauci,Anthony S. Fauci,Randi Y. Leavitt,Randi Y. Leavitt,Robert W. Lightfoot,Robert W. Lightfoot,Dennis J. McShane,Dennis J. McShane,John A. Mills,John A. Mills,Mary Betty Stevens,Mary Betty Stevens,Stanley L. Wallace,Nathan J. Zvaifler,Nathan J. Zvaifler +29 more
TL;DR: Criteria for the classification of Churg-Strauss syndrome were developed by comparing 20 patients who had this diagnosis with 787 control patients with other forms of vasculitis, and advantages of the traditional format compared with the classification tree format are discussed.
Journal ArticleDOI
Churg-Strauss Syndrome. Clinical Study and Long-Term Follow-Up of 96 Patients
TL;DR: The long-term prognosis of CSS is good and does not differ from that of polyarteritis nodosa, although most patients need low doses of oral corticosteroids for persistent asthma, even many years after clinical recovery from vasculitis.
Journal ArticleDOI
Long‐term followup of polyarteritis nodosa, microscopic polyangiitis, and Churg‐Strauss syndrome: Analysis of four prospective trials including 278 patients
M. Gayraud,Loïc Guillevin,Philippe Le Toumelin,Pascal Cohen,François Lhote,Philippe Casassus,Bernard Jarrousse +6 more
TL;DR: Rates of mortality due to PAN (related or unrelated to HBV), MPA, and CSS reflected disease severity and were higher than the mortality rate in the general population, and it is recommended that the intensity of the initial treatment be consistent with the severity of the disease.
Journal ArticleDOI
Epidemiology of systemic vasculitis: A ten‐year study in the United Kingdom
TL;DR: In the study population, the annual incidence of PSV is slowly increasing with time and the incidence is greatest in the elderly, with an overall peak in the 65-74 age group.