Estenosis subglótica y granulomatosis con poliangeítis (Wegener) en dos casos: Report of two cases
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TLDR
It is reported that two females aged 40 and 52 years, admitted to the hospital with a subglottic tracheal stenosis, responded to rituximab and required a tracheostomy.Abstract:
Granulomatosis with polyangiitis (GPA) or Wegener's disease is characterized by a granulomatous vasculitis of the upper and lower airways and kidney. It involves the lower respiratory tract causing subglottic tracheal stenosis, which occurs in approximately 22% of patients. We report two females aged 40 and 52 years, admitted to the hospital with a subglottic tracheal stenosis. Their symptoms and management are reviewed. The frst patient responded to rituximab. The second patient required a tracheostomy.read more
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Estenosis subglótica en granulomatosis con poliangitis (granulomatosis de Wegener): presentación de 4 casos
Gabriel Horta-Baas,María Fernanda Hernández-Cabrera,Rocío Catana,Mario Pérez-Cristóbal,Leonor A Barile-Fabris +4 more
TL;DR: La ESG presenta una alta morbilidad y la dilatacion endoscopica proporciona alivio sintomatico; sin embargo, suelen existir recidivas de la estenosis.
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Actualización en el estudio de Granulomatosis con poliangeitis (Granulomatosis de Wegener)
David Ladrón de Guevara,Felipe Pizarro Cerda,María Ángela Carreño,Antonio Piottante,Patricia Bitar +4 more
TL;DR: La granulomatosis con poliangeitis (GPA) es una vasculitis de pequeno vaso de caracter sistemico, that afecta mas frecuentemente el tracto respiratorio y el rinon, y se basa en terapia corticoidea e inmunosupresora.
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Estenosis bronquiales web-like secundarias a granulomatosis con poliangeitis
TL;DR: La granulomatosis con poliangeítis (GPA, Wegener’s), es una vasculitis sistémica that afecta característicamente al área otorrinolaringológica y vías respiratorias y se puede complicar con estenosis traqueobronquiales.
Granulomatosis de Wegener mimetizando una lesión tumoral de vértice de pulmón. Reporte de un caso clínico y revisión de la literatura
Gil Alberto Reyes Llerena,Rafael Frías Pita,Pablo Mateo Díaz,Niuvys Basulto Quiroz,Gil Reyes Guibert,José Antonio Martínez Quezada,Daysi Acosta Lapera,D. Carrillo Lovet +7 more
TL;DR: Se trata of un raro caso de granulomatosis de Wegener cuya forma of debut hizo plantear el diagnostico inicial de una lesion tumoral de vertice de pulmon.
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