Daniela Gerent Petry Piotto

TL;DR: The IRG-S expands the diagnostic armamentarium in evaluating USAIDs and points to different pathways regulating IRG expression as well as 3 additional autoinflammatory diseases: IL-18-mediated PAP and recurrent MAS, NEMO∆5-associated autoinflammatory syndrome (NEMO-NDAS), and SAMD9L- associated autoinflammatory disease (SAMD 9L-SAAD).

TL;DR: No risk factors for calcinosis were identified in this study, although that complication was found in half of the patients with juvenile dermatomyositis studied.

TL;DR: Recommendations, primarily based on consensus opinion, were agreed regarding investigation and monitoring of children who present with Raynaud's syndrome and further prospective studies are needed to better define the risk factors for progression to connective tissue disease.

TL;DR: Almost 10% of cSLE patients had symptomatic PA at diagnosis, particularly endocrine autoimmune disorders and antiphospholipid syndrome, and it is necessary to determine if this subgroup of c SLE patients have a distinct genetic background with a less severe disease and a better long-term outcome.

TL;DR: Evans syndrome in childhood‐onset systemic lupus erythematosus (cSLE) patients has been rarely reported and limited to small populations.