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Wilson Marques

Researcher at University of São Paulo

Publications -  121
Citations -  4080

Wilson Marques is an academic researcher from University of São Paulo. The author has contributed to research in topics: Ataxia & Medicine. The author has an hindex of 25, co-authored 109 publications receiving 3336 citations. Previous affiliations of Wilson Marques include Louisiana State University & University of London.

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Mutations in ADAR1 cause Aicardi-Goutières syndrome associated with a type I interferon signature

Gillian I. Rice, +53 more
- 01 Nov 2012 - 
TL;DR: It is shown that mutations in ADAR1 cause the autoimmune disorder Aicardi-Goutières syndrome (AGS), and it is speculated that ADar1 may limit the cytoplasmic accumulation of the dsRNA generated from genomic repetitive elements.
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Multi-system neurological disease is common in patients with OPA1 mutations

TL;DR: It is shown that extra-ocular neurological complications are common in OPA1 disease, and affect up to 20% of all mutational carriers, and careful surveillance is mandatory to optimize the detection and management of neurological disability in a group of patients who already have significant visual impairment.
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Assessment of interferon-related biomarkers in Aicardi-Goutières syndrome associated with mutations in TREX1, RNASEH2A, RNASEH2B, RNASEH2C, SAMHD1, and ADAR: a case-control study

Gillian I. Rice, +56 more
- 01 Dec 2013 - 
TL;DR: AGS is consistently associated with an interferon signature, which is apparently sustained over time and can thus be used to differentiate patients with AGS from controls, and neutralisation assays suggested that measurable antiviral activity was related toInterferon α production.
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The phenotypic manifestations of chromosome 17p11.2 duplication.

TL;DR: It is concluded that the possession of two copies of the peripheral myelin protein 22 gene within the duplicated region on chromosome 17p gives rise to a range of phenotypes and not solely to a CMT syndrome, and that the pattern of histological change in the peripheral nerves alters with advance of the disease.