E
Elijah R. Behr
Researcher at St George’s University Hospitals NHS Foundation Trust
Publications - 314
Citations - 14605
Elijah R. Behr is an academic researcher from St George’s University Hospitals NHS Foundation Trust. The author has contributed to research in topics: Brugada syndrome & Sudden cardiac death. The author has an hindex of 52, co-authored 274 publications receiving 11337 citations. Previous affiliations of Elijah R. Behr include University of London & St. George's University.
Papers
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Journal ArticleDOI
Sudden Death Can Be the First Manifestation of Hypertrophic Cardiomyopathy: Data From a United Kingdom Pathology Registry.
Gherardo Finocchiaro,Michael Papadakis,Gaia Tanzarella,Harshil Dhutia,Chris Miles,Maite Tome,Elijah R. Behr,Sanjay Sharma,Mary N. Sheppard +8 more
TL;DR: An inherited cardiomyopathy that is characterized by left ventricular hypertrophy, myocyte disarray at histology, and a propensity for fatal cardiac arrhythmias is described.
Journal ArticleDOI
Sex-Related Differences in Cardiac Channelopathies: Implications for Clinical Practice.
Babken Asatryan,Lauren Yee,Yael Ben-Haim,Stephan Dobner,Helge Servatius,Laurent Roten,Hildegard Tanner,Lia Crotti,Jonathan R. Skinner,Jonathan R. Skinner,Carol Ann Remme,Philippe Chevalier,Argelia Medeiros-Domingo,Elijah R. Behr,Elijah R. Behr,Tobias Reichlin,Katja E. Odening,Andrew D. Krahn +17 more
TL;DR: In this article, the authors provide a critical digest of the current evidence for sex-related differences in cardiac channelopathies and emphasize their clinical implications and remaining gaps requiring further research.
Journal ArticleDOI
Investigation on Sudden Unexpected Death in the Young (SUDY) in Europe: results of the European Heart Rhythm Association Survey.
Elijah R. Behr,Elijah R. Behr,Chiara Scrocco,Chiara Scrocco,Arthur A.M. Wilde,Eloi Marijon,Eloi Marijon,Lia Crotti,Konstantinos Iliodromitis,Carol Ann Remme,Jedrzej Kosiuk,Irina Rudaka,Georgia Sarquella Brugada,Georgia Sarquella Brugada,Katie Frampton,Katie Frampton,Eric Schulze-Bahr,Kristine Jubele,Carlo de Asmundis,Nynke Hofman,Jacob Tfelt-Hansen,Jacob Tfelt-Hansen,Serge Boveda,Giulio Conte +23 more
TL;DR: The European Heart Rhythm Association (EHRA) survey as discussed by the authors investigated the current practice for the investigation of sudden unexplained death in the young (SUDY) amongst European countries and highlighted a significant heterogeneity of service provision and variable adherence to current recommendations.
Journal ArticleDOI
Cadherin 2-Related Arrhythmogenic Cardiomyopathy Prevalence and Clinical Features
Alice Ghidoni,Perry M. Elliott,Petros Syrris,Hugh Calkins,Cynthia A. James,Daniel P. Judge,Brittney Murray,Julien Barc,Vincent Probst,Jean-Jacques Schott,Jiang Ping Song,Richard N.W. Hauer,Edgar T. Hoorntje,Edgar T. Hoorntje,J. Peter van Tintelen,Eric Schulze-Bahr,Robert M. Hamilton,Kirti Mittal,Christopher Semsarian,Elijah R. Behr,Michael J. Ackerman,Cristina Basso,Gianfranco Parati,Davide Gentilini,Maria Christina Kotta,Bongani M. Mayosi,Peter J. Schwartz,Lia Crotti +27 more
TL;DR: In this paper, an inherited cardiac disease characterized by fibrofatty replacement of the right and left ventricle, often causing ventricular dysfunction and heart failure, is described.
Genetic association study of QT interval highlights role for calcium signaling pathways in myocardial repolarization
Dan E. Arking,Sara L. Pulit,Lia Crotti,Pim van der Harst,Patricia B. Munroe,Tamara T. Koopmann,Nona Sotoodehnia,Elizabeth J. Rossin,Michael Morley,Xinchen Wang,Andrew D. Johnson,Alicia Lundby,Daniel F. Gudbjartsson,Peter A. Noseworthy,Mark Eijgelsheim,Yuki Bradford,Kirill Tarasov,Marcus Dörr,Martina Miiller-Nurasyid,Annukka M. Lahtinen,Ilja M. Nolte,Albert V. Smith,Joshua C. Bis,Aaron Isaacs,Stephen Newhouse,Daniel S. Evans,Wendy S. Post,Daryl Waggott,Leo-Pekka Lyytikäinen,Andrew A. Hicks,Lewin Eisele,David Ellinghaus,Caroline Hayward,Pau Navarro,Sheila Ulivi,Toshiko Tanaka,David J. Tester,Stéphanie Chatel,Stefan Gustafsson,Meena Kumari,Richard W Morris,Åsa Torinsson Naluai,Sandosh Padmanabhan,Alexander Kluttig,Bernhard Strohmer,Andrie G. Panayiotou,María José Torres,Michael Knoflach,Jaroslav A. Hubacek,Kamil Slowikowski,Soumya Raychaudhuri,Runjun D. Kumar,Tamara B. Harris,Lenore J. Launer,Alan R. Shuldiner,Alvaro Alonso,Joel S. Bader,Georg Ehret,Hailiang Huang,W. H. Linda Kao,James B. Strait,Peter W. Macfarlane,Morris Brown,Mark J. Caulfield,Nilesh J. Samani,Florian Kronenberg,Johann Willeit,J. Gustav Smith,Karin Halina Greiser,Henriette E. Meyer zu Schwabedissen,Karl Werdan,Massimo Carella,Leopoldo Zelante,Susan R. Heckbert,Bruce M. Psaty,Jerome I. Rotter,Ivana Kolcic,Ozren Poagek,Alan F. Wright,Maura Griffin,Mark J. Daly,David O. Arnar,Hilma Holm,Unnur Thorsteinsdottir,Joshua C. Denny,Dan M. Roden,Rebecca L. Zuvich,Valur Emilsson,Andrew S. Plump,Martin G. Larson,Christopher J. O'Donnell,Xiaoyan Yin,Marco Bobboll,Adamo Pio d'Adamo,Annamaria Iorio,Gianfranco Sinagra,Angel Carracedo,Steven R. Cummings,Mike A. Nalls,Antti Jula,Kimmo Kontula,Annukka Marjamaa,Lasse Oikarinen,Markus Perola,Kimmo Porthan,Raimund Erbe,Per Hoffmann,Karl-Heinz Jöckel,Hagen Kälsch,Markus M. Nöthen,Marcel den Hoed,Ruth J. F. Loos,Dag S. Thelle,Christian Gieger,Thomas Meitinger,Siegfried Perz,Annette Peters,Hanna Pruchal,Moritz F. Sinner,Melanie Waldenberger,Rudolf A. de Boer,Lude Franke,Pieter A. van der Vleuten,Britt M. Beckmann,Eimo Martens,Abdennasser Bardail,Nynke Hofman,Arthur A.M. Wilde,Elijah R. Behr,Chrysoula Dalageorgou,John R. Giudicessi,Argelia Medeiros-Domingo,Julien Barc,Florence Kyndt,Vincent Probst,Alice Ghidoni,Roberto Insolia,Robert M. Hamilton,Stephen W. Scherer,Jeffrey Brandimarto,Kenneth B. Margulies,Christine E. Moravec,Fabiola M. Del Greco,Christian Fuchsberger,Jeffrey R. O'Connell,Wai K. Lee,Graham Watt,Harry Campbell,Sarah H. Wild,Nour Eddine El Mokhtari,Norbert Frey,Folkert W. Asselbergs,Irene Mateo Leach,Gerjan Navis,Maarten P. van den Berg,Dirk J. van Veldhuisen,Manolis Kellis,Bouwe P. Krijthe,Oscar H. Franco,Albert Hofman,Jan A. Kors,André G. Uitterlinden,Jacqueline C.M. Witteman,Lyudmyla Kedenko,Claudia Lamina,Ben A. Oostra,Gonçalo R. Abecasis,Edward G. Lakatta,Antonella Mulas,Marco Orru,David Schlessinger,Manuela Uda,Marcello Ricardo Paulista Markus,Uwe Völker,Harold Snieder,Tim D. Spector,Johan Ärnlöv,Lars Lind,Johan Sundström,Ann-Christine Syvänen,Mika Kivimäki,Mika Kähönen,Nina Mononen,I. T. Raitakari,Jorma Viikari,Vera Adamkova,Stefan Kiech,Maria Brion,Andrew N. Nicolaides,Bernhard Paulweber,Johannes Haerting,Anna F. Dominiczak,Fredrik Nyberg,Peter H. Whincup,Aroon D. Hingorani,Jean-Jacques Schott,Connie R. Bezzina,Erik Ingelsson,Luigi Ferrucci,Paolo Gaspariniin,James F. Wilson,Igor Rudan,Andre Franke,Thomas W. Miihleisen,Peter P. Pramstaller,Terho Lehtimäki,Andrew D. Paterson,Afshin Parsa,Yongmei Liu,Cornelia M. van Duijn,David S. Siscovick,Vilmundur Gudnason,Yalda Jamshidi,Veikko Salomaa,Stephan B. Felix,Serena Sanna,Marylyn D. Ritchie,Bruno H. Stricker,Karl Stefansson,Laurie A. Boyer,Thomas P. Cappola,Jesper V. Olsen,Kasper Lage,Peter J. Schwartz,Stefan Kääb,Aravinda Chakravarti,Michael J. Ackerman,Arne Pfeufer,Paul I.W. de Bakker,Christopher Newton-Cheh +229 more
TL;DR: The integration of common variant association, expression and orthogonal protein-protein interaction screens provides new insights into cardiac electrophysiology and identifies new candidate genes for ventricular arrhythmias, LQTS and SCD.