M
Manfred Hönig
Researcher at University of Ulm
Publications - 43
Citations - 2588
Manfred Hönig is an academic researcher from University of Ulm. The author has contributed to research in topics: Transplantation & Hematopoietic stem cell transplantation. The author has an hindex of 20, co-authored 41 publications receiving 2189 citations. Previous affiliations of Manfred Hönig include Boston Children's Hospital.
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Journal ArticleDOI
Regulated Expression of Nuclear Receptor RORγt Confers Distinct Functional Fates to NK Cell Receptor-Expressing RORγt+ Innate Lymphocytes
Cedric Vonarbourg,Arthur Mortha,Viet L. Bui,Viet L. Bui,Pedro P. Hernandez,Pedro P. Hernandez,Elina A. Kiss,Thomas Hoyler,Melanie Flach,Bertram Bengsch,Robert Thimme,Christoph Hölscher,Manfred Hönig,Ulrich Pannicke,Klaus Schwarz,Carl F. Ware,Daniela Finke,Andreas Diefenbach +17 more
TL;DR: Using adoptive transfer of genetically tagged LTi-like cells, it is demonstrated that NKR⁻RORγt(+) innate lymphocytes but not NK cells were direct progenitors to NKR(+)RORγT(+) cells in vivo.
Journal ArticleDOI
Long-term outcome and lineage-specific chimerism in 194 patients with Wiskott-Aldrich syndrome treated by hematopoietic cell transplantation in the period 1980-2009: an international collaborative study
Daniele Moratto,Silvia Giliani,Carmem Bonfim,Evelina Mazzolari,Alain Fischer,Hans D. Ochs,Andrew J. Cant,Adrian J. Thrasher,Morton J. Cowan,Michael H. Albert,Trudy N. Small,Sung-Yun Pai,Elie Haddad,Antonella Lisa,Sophie Hambleton,Mary Slatter,Marina Cavazzana-Calvo,Nizar Mahlaoui,Capucine Picard,Troy R. Torgerson,Lauri Burroughs,Adriana Koliski,José Zanis Neto,Fulvio Porta,Waseem Qasim,Paul Veys,Kristina Kavanau,Manfred Hönig,Ansgar Schulz,Wilhelm Friedrich,Luigi D. Notarangelo +30 more
TL;DR: In this article, the authors analyzed long-term outcome and donor cell engraftment in 194 patients with Wiskott-Aldrich syndrome (WAS) who have been treated by hematopoietic cell transplantation (HCT) in the period 1980-2009.
Journal ArticleDOI
DOCK8 Deficiency: Clinical and Immunological Phenotype and Treatment Options - a Review of 136 Patients
S. Aydin,Sara Sebnem Kilic,Caner Aytekin,Ashish R Kumar,Oscar Porras,Leena Kainulainen,Larysa Kostyuchenko,Ferah Genel,Necil Kutukculer,Neslihan Edeer Karaca,Luis Ignacio Gonzalez-Granado,Jordan K. Abbott,Daifulah Al-Zahrani,Nima Rezaei,Zeina Baz,Jens Thiel,Jens Thiel,Stephan Ehl,László Maródi,Jordan S. Orange,Julie Sawalle-Belohradsky,Sevgi Keles,Steven M. Holland,Ozden Sanal,Deniz Cagdas Ayvaz,Ilhan Tezcan,Hamoud Al-Mousa,Zobaida Alsum,Abbas Hawwari,Ayse Metin,Susanne Matthes-Martin,Manfred Hönig,Ansgar Schulz,Capucine Picard,Capucine Picard,Vincent Barlogis,Andrew R. Gennery,Marianne Ifversen,Joris M. van Montfrans,Taco W. Kuijpers,Robbert G. M. Bredius,Gregor Dückers,Waleed Al-Herz,Sung-Yun Pai,Sung-Yun Pai,Raif S. Geha,Gundula Notheis,Carl Philipp Schwarze,Betul Tavil,Fatih Mehmet Azik,Kirsten Bienemann,Bodo Grimbacher,Bodo Grimbacher,Valerie Heinz,H. Bobby Gaspar,Roland C. Aydin,Beate Hagl,Benjamin Gathmann,Bernd H. Belohradsky,Hans D. Ochs,Talal A. Chatila,Ellen D. Renner,Helen Su,Alexandra F. Freeman,Karin R. Engelhardt,Karin R. Engelhardt,Michael H. Albert +66 more
TL;DR: A comprehensive evaluation of the clinical phenotype of DOCK8 deficiency in the largest cohort reported so far demonstrates the severity of the disease with relatively poor prognosis and early HSCT should be strongly considered as a potential curative measure.
Journal ArticleDOI
Reticular dysgenesis (aleukocytosis) is caused by mutations in the gene encoding mitochondrial adenylate kinase 2
Ulrich Pannicke,Manfred Hönig,Manfred Hönig,Isabell Hess,Claudia Friesen,Karlheinz Holzmann,Eva-Maria Rump,Thomas F. E. Barth,Markus Rojewski,Markus Rojewski,A. Schulz,Thomas Boehm,W. Friedrich,Klaus Schwarz +13 more
TL;DR: Reticular dysgenesis is the first example of a human immunodeficiency syndrome that is causally linked to energy metabolism and that can therefore be classified as a mitochondriopathy, and in vivo evidence for AK2 selectivity in leukocyte differentiation is provided.
Journal ArticleDOI
Outcome of hematopoietic stem cell transplantation for adenosine deaminase–deficient severe combined immunodeficiency
A Hassan,Claire Booth,Alex Brightwell,Zoe Allwood,Paul Veys,Kanchan Rao,Manfred Hönig,Wilhelm Friedrich,Andrew R. Gennery,Mary Slatter,Robbert G. M. Bredius,Andrea Finocchi,Caterina Cancrini,Alessandro Aiuti,Fulvio Porta,Arnalda Lanfranchi,Michela Ridella,Colin G. Steward,Alexandra H. Filipovich,Rebecca A. Marsh,Victoria Bordon,Saleh Al-Muhsen,Hamoud Al-Mousa,Zobaida Alsum,Hasan Al-Dhekri,Abdulaziz Al Ghonaium,Carsten Speckmann,Alain Fischer,Nizar Mahlaoui,Kim E. Nichols,Eyal Grunebaum,Daifulah Al Zahrani,Chaim M. Roifman,Jaap Jan Boelens,E. Graham Davies,Marina Cavazzana-Calvo,Luigi D. Notarangelo,H. Bobby Gaspar +37 more
TL;DR: HCT from matched sibling and family donors (MSDs, MFDs) had significantly better overall survival and Humoral immunity and donor B-cell engraftment was achieved in nearly all evaluable surviving patients and was seen even after unconditioned HCT.