An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-Based Guidelines for Diagnosis and Management
Ganesh Raghu,Harold R. Collard,Jim J. Egan,Fernando J. Martinez,Juergen Behr,Kevin K. Brown,Thomas V. Colby,Jean-François Cordier,Kevin R. Flaherty,Joseph A. Lasky,David A. Lynch,Jay H. Ryu,Jeffrey J. Swigris,Athol U. Wells,Julio Ancochea,Demosthenes Bouros,Carlos Roberto Ribeiro de Carvalho,Ulrich Costabel,Masahito Ebina,David M. Hansell,Takeshi Johkoh,Dong Soon Kim,Talmadge E. King,Yasuhiro Kondoh,Jeffrey L. Myers,Nestor L. Müller,Andrew G. Nicholson,Luca Richeldi,Moisés Selman,Rosalind F. Dudden,Barbara S. Griss,Shandra Protzko,Holger J. Schünemann +32 more
TLDR
This document represents the current state of knowledge regarding idiopathic pulmonary fibrosis, and contains sections on definition and epidemiology, risk factors, diagnosis, natural history, staging and prognosis, treatment, and monitoring disease course.Abstract:
This document is an international evidence-based guideline on the diagnosis and management of idiopathic pulmonary fibrosis, and is a collaborative effort of the American Thoracic Society, the European Respiratory Society, the Japanese Respiratory Society, and the Latin American Thoracic Association. It represents the current state of knowledge regarding idiopathic pulmonary fibrosis (IPF), and contains sections on definition and epidemiology, risk factors, diagnosis, natural history, staging and prognosis, treatment, and monitoring disease course. For the diagnosis and treatment sections, pragmatic GRADE evidence-based methodology was applied in a question-based format. For each diagnosis and treatment question, the committee graded the quality of the evidence available (high, moderate, low, or very low), and made a recommendation (yes or no, strong or weak). Recommendations were based on majority vote. It is emphasized that clinicians must spend adequate time with patients to discuss patients' values and preferences and decide on the appropriate course of action.read more
Citations
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Qualitative European survey of patients with idiopathic pulmonary fibrosis: patients’ perspectives of the disease and treatment
TL;DR: The findings demonstrate the value of seeking patients’ perspectives of a chronic disease such as IPF and how this information can be used to guide improvements in care, to best support the needs of patients with this devastating condition.
Journal ArticleDOI
Cryobiopsy in the Diagnosis of Diffuse Interstitial Lung Disease: Yield and Cost-Effectiveness Analysis
Fernanda Hernandez-Gonzalez,Carmen M. Lucena,José Ramírez,Marcelo Sánchez,María José Jiménez,Antoni Xaubet,Jacobo Sellares,Carlos Agustí +7 more
TL;DR: Cryobiopsy is a safe and potentially useful technique in the diagnostic assessment of patients with ILD and the systematic use of cryobiopsy has an important economic impact.
Journal ArticleDOI
Role of MicroRNAs in Lung Disease
TL;DR: The role of some miRNAs in different lung diseases as well as the possible future of these discoveries in clinical applications are discussed.
Journal ArticleDOI
Clinical diagnosis of idiopathic pleuroparenchymal fibroelastosis: A retrospective multicenter study.
Yasunori Enomoto,Yutaro Nakamura,Yasuomi Satake,Hiromitsu Sumikawa,Takeshi Johkoh,Thomas V. Colby,Hideki Yasui,Hironao Hozumi,Masato Karayama,Yuzo Suzuki,Kazuki Furuhashi,Tomoyuki Fujisawa,Noriyuki Enomoto,Naoki Inui,Toshihide Iwashita,Shigeki Kuroishi,Koshi Yokomura,Naoki Koshimizu,Mikio Toyoshima,Shiro Imokawa,Takashi Yamada,Toshihiro Shirai,Hiroshi Hayakawa,Takafumi Suda +23 more
TL;DR: Using a modified diagnostic criteria, relatively many patients with similar characteristics to those of idiopathic PPFE patients in the literature were recruited according to the modified criteria, and the possibility of clinical diagnosis of idiacurrent PPFE was considered.
Journal ArticleDOI
CT Features of the Usual Interstitial Pneumonia Pattern: Differentiating Connective Tissue Disease-Associated Interstitial Lung Disease From Idiopathic Pulmonary Fibrosis.
Jonathan H. Chung,Christian W. Cox,Steven M. Montner,Ayodeji Adegunsoye,Justin M. Oldham,Aliya N. Husain,Rekha Vij,Imre Noth,David A. Lynch,Mary E. Strek +9 more
TL;DR: Although UIP is usually associated with IPF, the index of suspicion for CTD-ILD should be raised in the care of patients with any of the three CT signs, and the highest specificity and sensitivity were seen for the straight-edge sign.
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TL;DR: The Diagnostic Process Is Dynamic Clinical Evaluation Radiological Evaluation Role of Surgical Lung Biopsy Unclassifiable Interstitial Pneumonia Bronchoalveolar Lavage Fluid Evaluation Idiopathic Pulmonary Fibrosis.
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