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Marcy E. MacDonald

Researcher at Harvard University

Publications -  322
Citations -  52277

Marcy E. MacDonald is an academic researcher from Harvard University. The author has contributed to research in topics: Huntington's disease & Huntingtin. The author has an hindex of 96, co-authored 315 publications receiving 49085 citations. Previous affiliations of Marcy E. MacDonald include Huntington's Disease Society of America & Ontario Institute for Cancer Research.

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Huntington's disease: the case for genetic modifiers

TL;DR: The search for genetic modifiers, much as the search for the HD gene did in the past, offers to open new entrées into the process of Huntington's disease pathogenesis by unlocking the biochemical changes that occur many years before diagnosis, and thereby providing validated target proteins and pathways for development of rational therapeutic interventions.
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The relationship between CAG repeat length and age of onset differs for Huntington's disease patients with juvenile onset or adult onset.

J. Michael Andresen, +96 more
TL;DR: In this article, a two-segment exponential regression model was proposed for age-of-obstinence analysis of the CAG repeat expansion in the HD gene, and a plot of natural log-transformed age of onset against CAG-repeat length revealed this segmental relationship.
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Thalamocortical neuron loss and localized astrocytosis in the Cln3Δex7/8 knock-in mouse model of Batten disease

TL;DR: Stereological analysis revealed a pronounced loss of neurons within individual laminae of somatosensory cortex of affected mice and the novel finding of a loss of sensory relay thalamic neurons in JNCL.
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Decreased association of the transcription factor Sp1 with genes downregulated in Huntington's disease.

TL;DR: It is found that mutant huntingtin dissociates Sp1 from target promoters, inhibiting transcription of specific genes in transgenic HD mouse brain, in striatal HD cells, and in human HD brain.
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The HTT CAG-Expansion Mutation Determines Age at Death but Not Disease Duration in Huntington Disease.

TL;DR: It is found that, as with clinical onset, HD age at death is determined by expanded CAG-repeat length and has no contribution from the normal CAG allele, and Surprisingly, disease duration is independent of the mutation's length.